{"orpha":100055,"name":"Acquired angioedema type 2","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["AAE 2","AAE II","Acquired angioneurotic edema type 2"],"definition":"A type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-100055/","orphanet_url":"https://www.orpha.net/en/disease/detail/100055","names":{"fr":{"name":"Angio-oedème acquis type II","synonyms":["AAE 2","AAE II","Angio-oedème bradykinique acquis type II","Oedème angioneurotique acquis type II"],"definition":"L'angioedème acquis de type 2 est une forme d'angioedème acquis (AOA) caractérisée par un oedème aigu des tissus sous-cutanés et sous-muqueux des viscères et/ou des voies aériennes supérieures."},"de":{"name":"Angioödem, erworbenes, Typ 2","definition":"Das Erworbene Angioödem Typ 2 (AAE2), eine Form des Erworbenen Angioödems (AAE; s. dort), ist gekennzeichnet durch akutes Ödem in subkutanen Geweben, inneren Organen und/oder oberen Atemwegen."},"es":{"name":"Angioedema adquirido tipo 2","synonyms":["Edema angioneurótico adquirido tipo 2","AAE II","AEA 2"],"definition":"Es un tipo de angioedema adquirido (AEA) caracterizado por un edema agudo en los tejidos subcutáneos, las vísceras y/o las vías aéreas superiores."},"it":{"name":"Angioedema acquisito, tipo 2","synonyms":["AAE 2","AAE II","Edema angioneurotico acquisito, tipo 2"],"definition":"L'angioedema acquisito tipo 2 (AAE 2) è un tipo di angioedema acquisito (si veda questo termine) caratterizzata da edema acuto nei tessuti sottocutanei, nei visceri e/o nelle vie respiratorie superiori."},"nl":{"name":"Verworven angio-oedeem type 2","synonyms":["AAE 2","AAE II","Verworven angioneurotisch oedeem type 2"],"definition":"Een type van verworven angio-oedeem, gekarakteriseerd door acuut oedeem in onderhuidse weefsels, ingewanden en/of de bovenste luchtwegen."},"pt":{"name":"Angioedema adquirido, tipo II"},"pl":{"name":"Nabyty obrzęk naczynioruchowy typu 2","synonyms":["AAE 2","AAE II","Nabyty obrzęk angioneurotyczny typu 2"]},"cs":{"name":"Získaný angioedém, typ 2","synonyms":["AAE 2","AAE II","Získaný angioneurotický edém, typ 2"]},"uk":{"name":"Набутий ангіоневротичний набряк, тип 2","synonyms":["AAE 2","AAE II","Набутий ангіоневротичний набряк 2 типу"],"definition":"A type of acquired angioedema (AAE) characterized by acute edema in subcutaneous tissues, viscera and/or the upper airway."},"zh":{"name":"获得性血管性水肿2型","synonyms":["获得性血管神经性水肿2型"],"definition":"获得性血管性水肿(AAE)的一种类型，以皮下组织、内脏和/或上呼吸道的急性水肿为特征。"},"tr":{"name":"Edinsel anjiyoödem tip 2","synonyms":["AAE 2","AAE II","Edinsel anjiyonörotik ödem tip 2"]}},"xrefs":[{"source":"ICD-10","code":"T78.3","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"4A00.15","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1071705004"},{"source":"MONDO","code":"0015055","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680381","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":528663,"name":"Acquired angioedema with C1Inh deficiency","classifications":[195]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[],"phenotypes":null}