ORPHA:100022

Extramedullary soft tissue plasmacytoma

This disease is described under Plasmacytoma

Names in Orphadata languages

12 of 12 languages

Lang	Name	Synonyms
en	Extramedullary soft tissue plasmacytoma
fr	Plasmacytome extramédullaire	PEM
de	Plasmozytom, extramedulläres (Weichteil-)
es	Plasmacitoma extramedular de tejidos blandos
it	Plasmocitoma extramidollare
nl	Extramedullair weke delen-plasmacytoom
pt	Plasmacitoma extramedular (tecidos moles)
pl	Pozaszpikowy szpiczak mnogi tkanek miękkich
cs	Extracelulární plazmocytom měkké tkáně
uk	Екстрамедулярна плазмоцитома мяких тканин
zh	髓外软组织浆细胞瘤
tr	Ekstramedüller yumuşak doku plazmasitoma

qualifier = Orphanet mapping relation

Source	Code	Qualifier	ICD relation	Validation
ICD-10	C90.2	NTBT	attributed	validated
ICD-11	2A83.2	NTBT	attributed	validated
MONDO	0015043	E		validated
UMLS	C2211567	E		validated

E exact · NTBT this ORPHAcode is narrower than the target · BTNT broader than the target · ND not decided.

Preferential parent (Orphanet linearisation):

Parents in the classifications (1):

ORPHA:86855Plasmacytoma
rare neurological diseases; rare hematological diseases; rare neoplastic diseases; rare transplant-related disorders

No children.

0 direct

Orphanet records no gene directly on this code.

1 record

Type	Class	Value	Area	Qualification	Validation	Source
Annual incidence	1-9 / 1 000 000	0.1 / 100 000	United States	Value and class	Validated	19016727[PMID]_SEER Surveillance Epidemiology and End Results 1992-2004[OTHER]

Value is Orphadata's ValMoy: the mean estimate per 100 000 for prevalence and incidence, the number of cases or families for case reports.

Orphanet has no HPO annotation for this code in this release.