{"orpha":100022,"name":"Extramedullary soft tissue plasmacytoma","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This disease is described under Plasmacytoma","url":"https://raremap.alftech.space/d/ORPHA-100022/","orphanet_url":"https://www.orpha.net/en/disease/detail/100022","names":{"fr":{"name":"Plasmacytome extramédullaire","synonyms":["PEM"]},"de":{"name":"Plasmozytom, extramedulläres (Weichteil-)"},"es":{"name":"Plasmacitoma extramedular de tejidos blandos"},"it":{"name":"Plasmocitoma extramidollare"},"nl":{"name":"Extramedullair weke delen-plasmacytoom"},"pt":{"name":"Plasmacitoma extramedular (tecidos moles)"},"pl":{"name":"Pozaszpikowy szpiczak mnogi tkanek miękkich"},"cs":{"name":"Extracelulární plazmocytom měkké tkáně"},"uk":{"name":"Екстрамедулярна плазмоцитома мяких тканин"},"zh":{"name":"髓外软组织浆细胞瘤"},"tr":{"name":"Ekstramedüller yumuşak doku plazmasitoma"}},"xrefs":[{"source":"ICD-10","code":"C90.2","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2A83.2","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0015043","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C2211567","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":86855,"name":"Plasmacytoma","classifications":[181,194,202,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.1,"area":"United States","status":"Validated","source":"19016727[PMID]_SEER Surveillance Epidemiology and End Results 1992-2004[OTHER]"}],"phenotypes":null}