{"orpha":99865,"name":"Spermatocytic seminoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Spermatocytic seminoma (SS) is an extremely rare form of testicular cancer distinguished from testicular seminomatous germ cell tumors by a very low rate of metastasis and lack of an ovarian equivalent.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-99865/","orphanet_url":"https://www.orpha.net/en/disease/detail/99865","names":{"fr":{"name":"Séminome spermatocytaire","definition":"Le séminome spermatocytaire est une forme extrêmement rare de cancer des testicules qui se distingue de la tumeur testiculaire germinale séminomateuse par un taux très bas de métastases et un manque d'équivalent ovarien."},"de":{"name":"Seminom, spermatozytisches"},"es":{"name":"Seminoma espermatocítico","definition":"Es una forma extremadamente infrecuente de cáncer testicular que se distingue de los tumores testiculares seminomatosos de células germinales por una tasa muy baja de metástasis y la ausencia de un equivalente ovárico."},"it":{"name":"Seminoma spermatocitico"},"nl":{"name":"Spermatocytisch seminoom","definition":"Spermatocytisch seminoom (SS) is een uiterst zeldzame vorm van teelbalkanker die zich van testiculaire seminomateuze kiemceltumoren (zie deze term) onderscheidt door een zeer lage uitzaaiingsgraad en het gebrek aan een equivalent in de eierstokken."},"pt":{"name":"Seminoma espermatocítico"},"pl":{"name":"Nasieniak spermatocytowy"},"cs":{"name":"Spermatocytický seminom"},"uk":{"name":"Сперматоцитарна семінома","definition":"Spermatocytic seminoma (SS) is an extremely rare form of testicular cancer distinguished from testicular seminomatous germ cell tumors (see this term) by a very low rate of metastasis and lack of an ovarian equivalent."},"zh":{"name":"精母细胞性精原细胞瘤","definition":"生精细胞精原细胞瘤(SS)是一种极其罕见的睾丸癌，与睾丸精原细胞瘤(见该术语)的区别在于转移率非常低，并且缺乏卵巢对应的肿瘤。"},"tr":{"name":"Spermatositik seminom"}},"xrefs":[{"source":"OMIM","code":"273300","qualifier":"NTBT","icd_relation":null,"validated":true},{"source":"ICD-10","code":"C62.9","qualifier":"NTBT","icd_relation":"index","validated":true},{"source":"ICD-11","code":"2C80.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"398146407"},{"source":"ICD-11","code":"XH80D1","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1589823811"},{"source":"MONDO","code":"0020513","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0334517","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10073118","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[{"type":"Referred to","orpha":99866,"name":"OBSOLETE: Metastatic spermatocytic seminoma","status":"inactive"}],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":363504,"name":"Germ cell tumor of testis","classifications":[185,202,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Unknown"],"onset":["Adolescent","Adult"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.03,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Europe","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}