{"orpha":99831,"name":"OBSOLETE: Common variable immunodeficiency due to an intrinsic T cell defect","type":"Etiological subtype","group":"Subtype of disorder","status":"inactive","flags":["Obsolete entity"],"synonyms":["OBSOLETE: CVID due to an intrinsic T cell defect"],"definition":null,"note":"This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Common variable immunodeficiency and related disorders","url":"https://raremap.alftech.space/d/ORPHA-99831/","orphanet_url":"https://www.orpha.net/en/disease/detail/99831","names":{"fr":{"name":"OBSOLETE : Déficit immunitaire commun variable dé à un défaut intrinsque des cellules T","synonyms":["OBSOLETE : CVID dû à un défaut intrinsèque des cellules T"]},"de":{"name":"OBSOLET: Immundefekt, allgemeiner variabler, durch intrinsischen T-Zell-Defekt","synonyms":["OBSOLET: CVID durch intrinsischen T-Zell-Defekt"]},"es":{"name":"OBSOLETO: Inmunodeficiencia común variable por defecto intrínseco de células T","synonyms":["OBSOLETO: IDCV por defecto intrínseco de células T"]},"it":{"name":"OBSOLETO: Immunodeficienza variabile comune da deficit intrinseco delle cellule T","synonyms":["OBSOLETO: CVID da deficit intrinseco delle cellule T"]},"nl":{"name":"OBSOLEET: Algemene variabele immuundeficiëntie door een intrinsiek T-celdefect","synonyms":["OBSOLEET: CVID door een intrinsiek T-celdefect"]},"pt":{"name":"OBSOLETO: Deficiência de proteína co-estimuladora induzível"},"pl":{"name":"NIEAKTUALNE: Pospolity zmienny Niedobór odpornosci z powodu wewnetrznego defektu komórek T","synonyms":["NIEAKTUALNE: CVID z powodu wewnętrznego defektu komórek T"]},"cs":{"name":"NEAKTUÁLNÍ: Common variable immunodeficiency due to an intrinsic T cell defect","synonyms":["OBSOLETE: CVID due to an intrinsic T cell defect"]},"uk":{"name":"ЗАСТАРІЛО: Загальний варіабельний імунодефіцит, зумовлений вродженим дефектом Т-лімфоцитів","synonyms":["ЗАСТАРІЛО: CVID внаслідок вродженого дефекту Т-лімфоцитів"]},"zh":{"name":"弃用：T细胞内在缺陷所致普通变异型免疫缺陷病","synonyms":["先天性T细胞缺陷所致CVID"]},"tr":{"name":"Eski adı: İntrinsik bir T hücresi defekti nedeniyle yaygın değişken immün yetmezlik","synonyms":["İntrinsik bir T hücresi defektine bağlı CVID"]}},"xrefs":[],"associations":[{"type":"Referred to","orpha":696851,"name":"Common variable immunodeficiency and related disorders"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}