{"orpha":99797,"name":"Anodontia","type":"Morphological anomaly","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"An extreme developmental dental anomaly characterized by the complete absence of all teeth.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-99797/","orphanet_url":"https://www.orpha.net/en/disease/detail/99797","names":{"fr":{"name":"Anodontie"},"de":{"name":"Anodontie"},"es":{"name":"Anodoncia","definition":"Es una anomalía extrema del desarrollo dental caracterizada por la ausencia total de dientes."},"it":{"name":"Anodontia"},"nl":{"name":"Anodontie","definition":"Een extreme afwijking van de tandontwikkeling, gekarakteriseerd door volledige afwezigheid van alle tanden."},"pt":{"name":"Anodontia"},"pl":{"name":"Anodoncja"},"cs":{"name":"Anodoncie"},"uk":{"name":"Анодонтія","definition":"An extreme developmental dental anomaly characterized by the complete absence of all teeth."},"zh":{"name":"先天性无齿症","definition":"无齿症是一种极端的牙齿发育异常，其特征是所有牙齿完全缺失。"},"tr":{"name":"Anodonti"}},"xrefs":[{"source":"OMIM","code":"206780","qualifier":"E","icd_relation":null,"validated":true},{"source":"ICD-10","code":"K00.0","qualifier":"E","icd_relation":"specific","validated":true},{"source":"ICD-11","code":"LA30.0","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"413433873"},{"source":"MONDO","code":"0008797","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D000848","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0399352","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"5818","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10002583","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98026,"name":"Rare odontologic disease"},"parents":[{"orpha":420755,"name":"Rare genetic odontal or periodontal disorder","classifications":[156]},{"orpha":164001,"name":"Rare odontal or periodontal disorder","classifications":[197]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}