{"orpha":93292,"name":"Adenoma of pancreas","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Pancreatic adenoma"],"definition":"A rare, benign tumor of the pancreas characterized by variable number and size of the cysts lined with glycogen rich epithelial cells. Clinical manifestation may include epigastric or abdominal pain, weight loss, diabetes, jaundice and palpable abdominal mass. Some patients have no symptoms and the tumor is discovered incidentally.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-93292/","orphanet_url":"https://www.orpha.net/en/disease/detail/93292","names":{"fr":{"name":"Adénome du pancréas","synonyms":["Adénome pancréatique"],"definition":"Tumeur rare bénigne du pancréas caractérisée par des kystes variant en nombre et taille, bordés de cellules épithéliales riches en glycogène. Les manifestations cliniques peuvent inclure des douleurs épigastriques ou abdominales, une perte de poids, un diabète, un ictère et une masse abdominale palpable. Certains patients ne présentant aucun symptôme, la tumeur est dans ce cas découverte de manière fortuite."},"de":{"name":"Adenom des Pankreas","synonyms":["Pankreasadenom"]},"es":{"name":"Adenoma de páncreas","synonyms":["Adenoma pancreático"],"definition":"Es un tumor de páncreas benigno y poco frecuente caracterizado por una variedad, en número y tamaño, de quistes revestidos por células epiteliales ricas en glucógeno. Las manifestaciones clínicas pueden incluir dolor epigástrico o abdominal, pérdida de peso, diabetes, ictericia y masa abdominal palpable. Algunos afectados son asintomáticos y el tumor es detectado de manera incidental."},"it":{"name":"Adenoma del pancreas","synonyms":["Adenoma pancreatico"],"definition":"L'adenoma del pancreas è una neoplasia benigna rara del pancreas, caratterizzata da cisti, di numero e dimensioni variabili, rivestite da cellule epiteliali ricche di glicogeno. I segni clinici comprendono il dolore epigastrico o addominale, la perdita di peso, il diabete, l'ittero e la presenza di una massa addominale palpabile. Alcuni pazienti sono asintomatici e il tumore viene diagnosticato casualmente."},"nl":{"name":"Adenoom van pancreas","synonyms":["Adenoom van alvleesklier","Pancreasadenoom","Pancreatisch adenoom"],"definition":"Een zeldzame, goedaardige tumor van de pancreas, gekarakteriseerd door cysten die variabel zijn in aantal en omvang en die bekleed zijn met epitheelcellen rijk aan glycogeen. Mogelijke klinische manifestaties zijn onder meer epigastrische of abdominale pijn, gewichtsverlies, diabetes, geelzucht en een tastbare abdominale massa. Sommige patiënten hebben geen symptomen en de tumor wordt toevallig ontdekt."},"pt":{"name":"Adenoma pancreático"},"pl":{"name":"Gruczolak trzustki","synonyms":["Pancreatic adenoma"]},"cs":{"name":"Adenom pankreatu","synonyms":["Pankreatický adenom"]},"uk":{"name":"Аденома підшлункової залози","synonyms":["Аденома підшлункової залози"],"definition":"A rare, benign tumor of the pancreas characterized by variable number and size of the cysts lined with glycogen rich epithelial cells. Clinical manifestation may include epigastric or abdominal pain, weight loss, diabetes, jaundice and palpable abdominal mass. Some patients have no symptoms and the tumor is discovered incidentally."},"zh":{"name":"胰腺腺瘤","synonyms":["胰腺腺瘤"],"definition":"一种罕见的良性胰腺肿瘤，其特征是数目和大小不一的囊肿，内衬富含糖原的上皮细胞。临床表现包括上腹部或腹部疼痛、体重减轻、糖尿病、黄疸和可触及的腹部肿块。有些患者没有症状，肿瘤被偶然发现。"},"tr":{"name":"Pankreas adenomu","synonyms":["Pankreas adenomu"]}},"xrefs":[{"source":"ICD-10","code":"D13.6","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2E92.8","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1870352651"},{"source":"MONDO","code":"0019668","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"C538110","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1142432","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"4204","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10058902","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":165711,"name":"Rare abdominal surgical disease","classifications":[182]},{"orpha":424033,"name":"Rare epithelial tumor of pancreas","classifications":[152,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult","Elderly"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}