{"orpha":90394,"name":"Discrete papular lichen myxedematosus","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Discrete papular lichen myxedematosus is a rare chronic, slowly progressive form of localized lichen myxedematosus characterized by the development of a few to multiple small symmetrical skin-coloured mucinous papules on the limbs and trunk.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-90394/","orphanet_url":"https://www.orpha.net/en/disease/detail/90394","names":{"fr":{"name":"Lichen myxoedémateux discret","definition":"Le lichen myxoedémateux discret est une forme rare, chronique et lentement progressive de lichen myxoedémateux localisé caractérisée par le développement de peu ou de nombreuses petites papules mucineuses symétriques couleur chair sur les membres et le tronc."},"de":{"name":"Lichen myxoedematosus, diskreter papulöser","definition":"Der Diskrete papuläre Lichen myxoedematosus ist eine seltene chronische, langsam progrediente Form des lokalisierten Lichen myxoedematosus (s. dort) und gekennzeichnet durch die Entwicklung von wenigen bis vielen kleinen symmetrischen hautfarbenen muzinösen Papeln an Gliedmassen und Stamm."},"es":{"name":"Liquen mixedematoso papular discreto","definition":"El liquen mixedematoso papular discreto es una forma crónica poco frecuente y de progreso lento de liquen mixedematoso localizado (consulte este término) que se caracteriza por el desarrollo de pocos a múltiples pequeñas pápulas mucinosas color piel simétricamente ubicadas en extremidades y tronco."},"it":{"name":"Lichen mixedematoso papuloso, forma discreta","definition":"Il lichen mixedematoso papuloso discreto è una forma cronica rara, a progressione lenta del lichen mixedematoso localizzato (si veda questo termine), caratterizzata dallo sviluppo di poche-numerose piccole papule mucinose simmetriche color carne sugli arti e sul tronco."},"nl":{"name":"Discrete papulaire lichen myxoedematosus","definition":"Een zeldzame chronische, traag progressieve vorm van gelokaliseerde lichen myxoedematosus, gekenmerkt door ontwikkeling van enkele tot vele kleine symmetrische huidkleurige mucineuze papels op ledematen en romp."},"pt":{"name":"Líquen mixedematoso papular, discreto"},"pl":{"name":"Liszaj śluzowaty dyskretna odmiana grudkowa"},"cs":{"name":"Diskrétní papulární myxedematózní lichen"},"uk":{"name":"Дискретний папульозний лишай мікседематозний","definition":"Discrete papular lichen myxedematosus is a rare chronic, slowly progressive form of localized lichen myxedematosus (see this term) characterized by the development of a few to multiple small symmetrical skin-coloured mucinous papules on the limbs and trunk."},"zh":{"name":"散发性丘疹性粘液水肿性苔癣"},"tr":{"name":"Ayrık papüler liken miksödemöz"}},"xrefs":[{"source":"ICD-10","code":"L98.5","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"EB90.11","qualifier":"NTBT","icd_relation":"attributed","validated":true,"icd11_uri":"null"},{"source":"MONDO","code":"0019579","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4273967","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":86795,"name":"Localized lichen myxedematosus","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}