{"orpha":84085,"name":"Hinman syndrome","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["HAS","HS","Hinman-Allen syndrome","Non-neurogenic neurogenic bladder","Occult neuropathic bladder"],"definition":"Hinman syndrome (HS) or non-neurogenic neurogenic bladder is a voiding dysfunction of the bladder of neuropsychological origin that is characterized by functional bladder outlet obstruction in the absence of neurologic deficits.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-84085/","orphanet_url":"https://www.orpha.net/en/disease/detail/84085","names":{"fr":{"name":"Syndrome de Hinman","synonyms":["Dyssynergie vésico-sphinctérienne fonctionnelle","HAS","HS","Neuro-vessie non neurogène","Neuro-vessie occulte","Syndrome de Hinman-Allen","Vessie neurogène non neurogène","Vessie neurologique non neurologique et non neurogène"],"definition":"Le syndrome de Hinman ou vessie neurogène non-neurogène est un dysfonctionnement de l'évacuation de la vessie d'origine neuropsychologique caractérisée par une obstruction vésicale fonctionnelle en l'absence de déficit neurologique."},"de":{"name":"Hinman-Syndrom","synonyms":["HAS","HS","Hinman-Allen-Syndrom","Nicht-neurogene neurogene Blase","Okkulte neurogene Blase"],"definition":"Das Hinman-Syndrom (HS) oder nicht-neurogene neurogene Blase ist eine Entleerungsstörung der Blase mit neuropsychologischen Ursachen. Das Syndrom ist gekennzeichnet durch eine funktionelle Obstruktion des Blasenausgangs ohne neurologische Auffälligkeiten."},"es":{"name":"Síndrome de Hinman","synonyms":["HAS","HS","Síndrome de Hinman-Allen","Vejiga neurogénica no neurogénica","Vejiga neuropática oculta"],"definition":"El síndrome de Hinman (SH) o vejiga neurógena no neurogénica es una disfunción miccional de la vejiga de origen neuropsicológico que se caracteriza por una obstrucción funcional de la salida de la vejiga en ausencia de déficits neurológicos."},"it":{"name":"Sindrome di Hinman","synonyms":["Vescica neurogena non neurogena","Vescica neuropatica occulta","HAS","HS","Sindrome di Hinman-Allen"],"definition":"La sindrome di Hinman (HS) o vescica neurogena non neurogena è una disfunzione dello svuotamento della vescica di origine neuropsicologica, che si caratterizza per l'ostruzione funzionale dello sbocco vescicale in assenza di deficit neurologici."},"nl":{"name":"Syndroom van Hinman","synonyms":["HAS","HS","Niet-neurogene overactieve blaas","Occulte neuropathische blaas","Syndroom van Hinman-Allen"],"definition":"Hinmansyndroom (HS) of niet-neurogene overactieve blaas is een mictiestoornis van de blaas van neuropsychologische oorsprong, die wordt gekenmerkt door een functionele obstructie van de blaas in afwezigheid van neurologische gebreken."},"pt":{"name":"Síndrome Hinman","synonyms":["Bexiga neurogénica não neurogénica","HAS","HS","Síndrome Hinman-Allen"],"definition":"A Síndrome de Hinman (SH) ou bexiga neurogénica não-neurogénica é uma disfunção miccional da bexiga de origem neuropsicológica que é caracterizada por obstrução funcional do fluxo de saída da bexiga na ausência de défices neurológicos."},"pl":{"name":"Zespół Hinmana","synonyms":["HAS","HS","Nieneurogenny-neurogenny pęcherz moczowy","Zespół Hinmana","Zespół Hinmana i Allena"]},"cs":{"name":"Hinmanův syndrom","synonyms":["HAS","HS","Hinmanův-Allenův syndrom","Non-neurogenní neurogenní měchýř","Okultní neuropatický měchýř","Hinman-Allenův syndrom"]},"uk":{"name":"Синдром Хінмана","synonyms":["HAS","Синдром Хінмана-Алена","HS","Ненейрогенний нейрогенний сечовий міхур","Окультний невропатичний сечовий міхур"],"definition":"Hinman syndrome (HS) or non-neurogenic neurogenic bladder is a voiding dysfunction of the bladder of neuropsychological origin that is characterized by functional bladder outlet obstruction in the absence of neurologic deficits."},"zh":{"name":"Hinman综合征","synonyms":["非神经性神经源性膀胱"]},"tr":{"name":"Hinman sendromu","synonyms":["HS","HAS","Hinman-Allen sendromu","Gizli nöropatik mesane","Nörojenik olmayan nörojenik mesane"]}},"xrefs":[{"source":"ICD-10","code":"N32.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"GC01.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"440438107"},{"source":"MONDO","code":"0019395","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1997362","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":101433,"name":"Rare urogenital disease"},"parents":[{"orpha":101433,"name":"Rare urogenital disease","classifications":[185]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":{"validation_status":"y","online":"y","validation_date":"2025-10-07","source":"38741815[PMID]","terms":[{"hpo":"HP:0032465","label":"Bladder trabeculation","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0040183","label":"Encopresis","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0000805","label":"Enuresis","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0000010","label":"Recurrent urinary tract infections","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0008635","label":"Urinary bladder wall hypertrophy","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0000020","label":"Urinary incontinence","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0000016","label":"Urinary retention","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0000012","label":"Urinary urgency","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0000076","label":"Vesicoureteral reflux","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0002027","label":"Abdominal pain","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0002019","label":"Constipation","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0030157","label":"Flank pain","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0000126","label":"Hydronephrosis","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0002018","label":"Nausea","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0000083","label":"Renal insufficiency","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0100712","label":"Abnormal lumbar spine morphology","frequency":"Excluded (0%)","criteria":null}]}}