{"orpha":83484,"name":"St. Louis encephalitis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Saint Louis encephalitis"],"definition":"An acute arboviral infection caused by a virus of the <i>Flaviviridae</i> family transmitted by an infected mosquito, and characterized by the onset of flu-like symptoms such as fever, malaise, headache, cough, and sore throat that can progress to meningitis or encephalitis with symptoms like nausea, vomiting, confusion, stiff neck, disorientation, irritability, tremors, and convulsions. Photophobia, cranial nerve palsies, and even coma may occur.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-83484/","orphanet_url":"https://www.orpha.net/en/disease/detail/83484","names":{"fr":{"name":"Encéphalite de St. Louis","synonyms":["Encéphalite de Saint-Louis"],"definition":"Infection aiguë causée par un arbovirus de la famille des<i>Flaviviridae</i> transmis par un moustique infecté, caractérisée par l'apparition de symptômes de type fébrile tels que fièvre, malaise, maux de tête, toux et maux de gorge pouvant évoluer vers une méningite ou une encéphalite dont les symptômes sont des nausées, des vomissements, une confusion, une raideur de la nuque, une désorientation, une irritabilité, des tremblements et des convulsions. On peut par ailleurs observer une photophobie, une paralysie des nerfs crâniens, voire un coma."},"de":{"name":"St.-Louis-Enzephalitis"},"es":{"name":"Encefalitis de St. Louis","definition":"Es una infección arboviral aguda causada por un virus de la familia <i>Flaviviridae</i> transmitida por un mosquito infectado y caracterizada por la aparición de síntomas similares a la gripe, tales como fiebre, malestar general, cefalea, tos y dolor de garganta que pueden progresar a meningitis o encefalitis con síntomas como náuseas, vómitos, confusión, rigidez en el cuello, desorientación, irritabilidad, temblores y crisis epilépticas. También puede producirse fotofobia, parálisis de nervios craneales e incluso coma."},"it":{"name":"Encefalite di St Louis"},"nl":{"name":"Saint Louis-encefalitis","definition":"Een acute arbovirale infectie veroorzaakt door een virus van de <i>Flaviviridae</i>-familie en overgedragen door een geïnfecteerde mug. De infectie wordt gekarakteriseerd door aanvang van griepachtige symptomen zoals koorts, malaise, hoofdpijn, hoest, en keelpijn, en kan evolueren tot meningitis of encefalitis met symptomen als misselijkheid, braken, verwardheid, stijve nek, desoriëntatie, prikkelbaarheid, tremor, en convulsies. Fotofobie, hersenzenuwverlammingen, en zelfs coma kunnen voorkomen."},"pt":{"name":"Encefalite de St. Louis"},"pl":{"name":"Zapalenie mózgu St. Louis","synonyms":["Zapalenie mózgu Saint Louis"]},"cs":{"name":"Encefalitida St. Louis","synonyms":["Saint Louis encefalitida","Saintlouiská encefalitida"]},"uk":{"name":"Енцефаліт Сент-Луїса","synonyms":["Енцефаліт Сент-Луїса"],"definition":"An acute arboviral infection caused by a virus of the <i>Flaviviridae</i> family transmitted by an infected mosquito, and characterized by the onset of flulike symptoms such as fever, malaise, headache, cough, and sore throat that can progress to meningitis or encephalitis with symptoms like nausea, vomiting, confusion, stiff neck, disorientation, irritability, tremors, and convulsions. Photophobia, cranial nerve palsies, and even coma may occur."},"zh":{"name":"圣路易斯脑炎","synonyms":["圣路易斯脑炎"]},"tr":{"name":"St. Louis ensefaliti","synonyms":["Saint Louis ensefaliti"]}},"xrefs":[{"source":"ICD-10","code":"A83.3","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"1C86","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1306878274"},{"source":"MONDO","code":"0005969","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D004674","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0014060","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10041896","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":68416,"name":"Rare infectious disease"},"parents":[{"orpha":166490,"name":"Infectious disease with epilepsy","classifications":[181]},{"orpha":98252,"name":"Infectious encephalitis","classifications":[181,203]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.38,"area":"Europe","status":"Not yet validated","source":"ORPHANET"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}