{"orpha":79093,"name":"OBSOLETE: Foix-Alajouanine syndrome","type":"Malformation syndrome","group":"Disorder","status":"inactive","flags":["Obsolete entity"],"synonyms":["OBSOLETE: Angiodysgenetic necrotizing myelopathy","OBSOLETE: Familial osteosclerosis with abnormalities of the nervous system and meninges","OBSOLETE: Subacute angiohypertrophic myelomalacia","OBSOLETE: Subacute ascending necrotizing myelitis","OBSOLETE: Subacute necrotizing myelitis"],"definition":null,"note":"This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Spinal fast-flow vascular malformation","url":"https://raremap.alftech.space/d/ORPHA-79093/","orphanet_url":"https://www.orpha.net/en/disease/detail/79093","names":{"fr":{"name":"OBSOLETE : Syndrome de Foix-Alajouanine","synonyms":["OBSOLETE : Myélite ascendante nécrosante sub-aiguë","OBSOLETE : Myélopathie nécrotique subaiguë","OBSOLETE : Névrite nécrotique subaiguë","OBSOLETE : Ostéosclérose familiale avec anomalies du système nerveux et des méninges"]},"de":{"name":"OBSOLET: Foix-Alajouanine-Syndrom","synonyms":["OBSOLET: Subakute nekrotisierende Myelitis"]},"es":{"name":"OBSOLETO: Síndrome de Foix-Alajouanine","synonyms":["OBSOLETO: Osteosclerosis familiar con anomalías del sistema nervioso y de las meninges","OBSOLETO: Mielitis necrotizante ascendente subcutánea","OBSOLETO: Mielitis necrotizante subcutánea","OBSOLETO: Mielomalacia angiohipertrófica subcutánea","OBSOLETO: Mielopatía angiodisgenética necrotizante"]},"it":{"name":"OBSOLETO: Sindrome di Foix-Alajouanine","synonyms":["OBSOLETO: Mielopatia angiodisgenetica necrotizzante","OBSOLETO: Osteosclerosi familiare con anomalie del sistema nervoso e delle meningi","OBSOLETO: Mielite necrotizzante subacuta","OBSOLETO: Mielomalacia angioipertrofica subacuta","OBSOLETO: Mielite ascendente necrotizzante subacuta"]},"nl":{"name":"OBSOLEET: Syndroom van Foix-Alajouanine","synonyms":["NIET ZELDZAME ZIEKTE IN EUROPA: Angiodysgenetische necrotiserende myelopathie","NIET ZELDZAME ZIEKTE IN EUROPA: Familiale osteosclerose met afwijkingen van zenuwstelsel en meningen","NIET ZELDZAME ZIEKTE IN EUROPA: Subacute necrotiserende myelitis","NIET ZELDZAME ZIEKTE IN EUROPA: Subacute angiohypertrofische myelomalacie","NIET ZELDZAME ZIEKTE IN EUROPA: Subacute stijgende necrotiserende myelitis"]},"pt":{"name":"OBSOLETO: Síndrome Foix-Alajouanine","synonyms":["OBSOLETO: Mielopatia necrotizante angiodisgénica","OBSOLETO: Mielite necrotizante sub-aguda ascendente","OBSOLETO: Mielomalácia angio-hipertrófica sub-aguda","OBSOLETO: Mielite necrotizante sub-aguda","OBSOLETO: Malformação arterio-venosa espinhal"]},"pl":{"name":"NIEAKTUALNE: Zespół Foixa i Alajouanine","synonyms":["NIEAKTUALNE: Podostre martwicowe zapalenie szpiku","NIEAKTUALNE: Podostre wstępujące martwicowe zapalenie rdzenia","NIEAKTUALNE: Rodzinna osteoskleroza z nieprawidłowościami układu nerwowego i opon mózgowych"]},"cs":{"name":"NEAKTUÁLNÍ: Foixův-Alajouaninův syndrom","synonyms":["NEAKTUÁLNÍ: Angiodysgenetická nekrotizující myelopatie","NEAKTUÁLNÍ: Subakutní angiohypertrofická myelomalacie","NEAKTUÁLNÍ: Subakutní ascendentní nekrotizující myelitida","NEAKTUÁLNÍ: Subakutní nekrotizující myelitida","NEAKTUÁLNÍ: Familiární osteoskleróza s abnormalitami nervového systému a meningů","NEAKTUÁLNÍ: Foix-Alajouaninův syndrom"]},"uk":{"name":"Синдром Фуа-Алажуаніна","synonyms":["Ангіодисгенетична некротизуюча мієлопатія","Сімейний остеосклероз з ураженням нервової системи та мозкових оболонок","Підгостра ангіогіпертрофічна мієломаляція","Підгострий висхідний некротизуючий мієліт","Підгострий некротичний мієліт"],"definition":"Foix-Alajouanine syndrome, also called subacute ascending necrotising myelitis, results from chronic congestion of the extrinsic pial veins of the spinal cord and of the intrinsic subpial network. It is characterised by progressive ascending deficit over a period of several months or years."},"zh":{"name":"Foix-Alajouanine综合征","synonyms":["家族性骨硬化伴神经系统和脑膜异常"]},"tr":{"name":"Foix-Alajouanine sendromu","synonyms":["Subakut nekrotizan miyelit","Anjiyodisgenetik nekrotizan miyelopati","Subakut anjiyohipertrofik miyelomalazi","Subakut artan nekrotizan miyelit","Sinir sistemi ve meninks anormallikleri ile seyreden ailesel osteoskleroz"]}},"xrefs":[],"associations":[{"type":"Referred to","orpha":715025,"name":"Spinal fast-flow vascular malformation"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}