{"orpha":77303,"name":"OBSOLETE: Common variable immunodeficiency due to an intrinsic B cell defect","type":"Etiological subtype","group":"Subtype of disorder","status":"inactive","flags":["Obsolete entity"],"synonyms":["OBSOLETE: CVID due to an intrinsic B cell defect"],"definition":null,"note":"This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Common variable immunodeficiency and related disorders","url":"https://raremap.alftech.space/d/ORPHA-77303/","orphanet_url":"https://www.orpha.net/en/disease/detail/77303","names":{"fr":{"name":"OBSOLETE : Déficit immunitaire commun variable dé à un défaut intrinsque des cellules B","synonyms":["OBSOLETE : CVID dû à un défaut intrinsèque des cellules B"]},"de":{"name":"OBSOLET: Immundefekt, allgemeiner variabler, durch intrinsischen B-Zell-Defekt","synonyms":["OBSOLET: CVID durch intrinsischen B-Zell-Defekt"]},"es":{"name":"OBSOLETO: Inmunodeficiencia común variable por defecto intrínseco de las células B","synonyms":["OBSOLETO: IDCV por defecto intrínseco de células B"]},"it":{"name":"OBSOLETO: Immunodeficienza variabile comune da difetto intrinseco delle cellule B","synonyms":["OBSOLETO: CVID da difetto intrinseco delle cellule B"]},"nl":{"name":"OBSOLEET: Algemene variabele immuundeficiëntie als gevolg van een intrinsiek B cel-defect","synonyms":["OBSOLEET: CVID als gevolg van een intrinsiek B cel-defect"]},"pt":{"name":"OBSOLETO: Hipogamaglobulinemia por deficiência de CD19"},"pl":{"name":"NIEAKTUALNE: Powszechny zmienny Niedobór odpornosci z powodu wewnetrznego defektu komórek B","synonyms":["NIEAKTUALNE: CVID z powodu wewnętrznego defektu komórek B"]},"cs":{"name":"NEAKTUÁLNÍ: Common variable immunodeficiency due to an intrinsic B cell defect","synonyms":["OBSOLETE: CVID due to an intrinsic B cell defect"]},"uk":{"name":"ЗАСТАРІЛО: Простий варіабельний імунодефіцит, зумовлений вродженим дефектом В-клітин","synonyms":["ЗАСТАРІЛО: CVID внаслідок вродженого дефекту В-клітин"]},"zh":{"name":"弃用：内在B细胞缺陷所致常见变异型免疫缺陷病","synonyms":["固有B细胞缺陷所致CVID"]},"tr":{"name":"Eski adı: İntrinsik B hücresi defektine bağlı yaygın değişken immün yetmezlik","synonyms":["İntrinsik bir B hücresi defektine bağlı CVID"]}},"xrefs":[],"associations":[{"type":"Referred to","orpha":696851,"name":"Common variable immunodeficiency and related disorders"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}