{"orpha":764,"name":"Pyomyositis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Myositis purulenta tropica","Myositis tropicans","PM","Suppurative myositis","Tropical pyomyositis"],"definition":"Pyomyositis (PM) is a rare primary bacterial infection of the skeletal muscle, usually resulting from hematogenous spread or due to muscle injury, and characterized by pain and tenderness in the affected muscle, fever and abscess formation.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-764/","orphanet_url":"https://www.orpha.net/en/disease/detail/764","names":{"fr":{"name":"Pyomyosite","synonyms":["Myosite purulente tropicale","Myosite suppurative","Myosite tropicale","PM"],"definition":"La pyomyosite (PM) est une infection bactérienne primitive rare du muscle squelettique, résultant généralement d'une dissémination hématogène ou due à une blessure musculaire. Elle est caractérisée par une douleur et une sensibilité du muscle atteint, une fièvre et la formation d'abcès."},"de":{"name":"Pyomyositis","synonyms":["Myositis purulenta tropica","Myositis tropicans","Suppurative Myositis","Tropische Pyomyositis"],"definition":"Die Pyomyositis (PM) ist eine seltene, primär bakterielle Infektion des Skelettmuskels und resultiert meist aus hämatogener Streuung oder einer Verletzung des Muskels. Der betroffene Muskel schmerzt und ist druckempfindlich. Es besteht Fieber, Abszessbildung ist möglich."},"es":{"name":"Piomiositis","synonyms":["Miositis purulenta tropical","Miositis supurativa","Miositis tropical","Piomiositis tropical"],"definition":"La piomiositis (PM) es una rara infección bacteriana primaria del músculo esquelético, generalmente derivada de una diseminación hemática o debida a una lesión muscular, y se caracteriza por sensibilidad y dolor a la palpación en el músculo afectado, fiebre y formación de abscesos."},"it":{"name":"Piomiosite","synonyms":["Miosite purulenta tropicale","Miosite suppurativa","Miosite tropicale","PM","Piomiosite tropicale"],"definition":"La piomiosite (PM) è una rara infezione batterica primitiva del muscolo scheletrico, di solito da propagazione ematica o lesione del muscolo, caratterizzata da dolore e rammollimento del muscolo coinvolto, febbre e formazione di ascessi."},"nl":{"name":"Pyomyositis","synonyms":["Myositis purulenta tropica","Myositis tropicans","PM","Suppuratieve myositis","Tropische pyomyositis"],"definition":"Pyomyositis (PM) is een zeldzame, primaire bacteriële infectie van de skeletspieren die gewoonlijk het gevolg is van hematogene verspreiding of door een spierblessure, en die gekenmerkt wordt door pijn en gevoeligheid in de getroffen spier, koorts en abcesvorming."},"pt":{"name":"Piomiosite"},"pl":{"name":"Ropne zapalenie mięśni","synonyms":["Myositis purulenta tropica","PM","Ropne zapalenie mięśni","Tropikalne ropne zapalenie mięśni","Tropikalne zapalenie mięśni"],"definition":"Ropne zapalenie mięśni (Pyomyositis, PM) jest rzadkim pierwotnym zakażeniem bakteryjnym mięśnia szkieletowego, powstałym zwykle w wyniku krwiopochodnego rozprzestrzeniania lub w wyniku urazu mięśnia. Charakteryzuje się bólem i tkliwością dotkniętego mięśnia oraz gorączką i utworzeniem ropnia.inf brsup"},"cs":{"name":"Pyomyozitida","synonyms":["Myositis purulenta tropica","Tropická myozitida","PM","Supurativní myozitida","Tropická pyomyozitida"]},"uk":{"name":"Піоміозит","synonyms":["Тропічний гнійний міозит","Тропічний міозит","PM","Гнійний міозит","Тропічний піоміозит"],"definition":"Pyomyositis (PM) is a rare primary bacterial infection of the skeletal muscle, usually resulting from hematogenous spread or due to muscle injury, and characterized by pain and tenderness in the affected muscle, fever and abscess formation."},"zh":{"name":"化脓性肌炎","synonyms":["热带性脓性肌炎"]},"tr":{"name":"Pyomyozit","synonyms":["PM","Miyozit tropikanlar","Süpüratif miyozit","Tropikal piyomiyozit","Miyozit purulenta tropica"]}},"xrefs":[{"source":"ICD-10","code":"M60.0","qualifier":"NTBT","icd_relation":"inclusion","validated":true},{"source":"ICD-11","code":"FB30","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"856598467"},{"source":"MONDO","code":"0019168","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D052880","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0041188","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"4614","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10037652","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":68416,"name":"Rare infectious disease"},"parents":[{"orpha":163582,"name":"Rare bacterial infectious disease","classifications":[203]},{"orpha":182222,"name":"Rare systemic disease","classifications":[196]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":{"validation_status":"y","online":"y","validation_date":"2016-06-01","source":null,"terms":[{"hpo":"HP:0001945","label":"Fever","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0003326","label":"Myalgia","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0100614","label":"Myositis","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0100838","label":"Recurrent cutaneous abscess formation","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0001482","label":"Subcutaneous nodule","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0001974","label":"Increased total leukocyte count","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0002719","label":"Recurrent infections","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0100616","label":"Testicular teratoma","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0001824","label":"Weight loss","frequency":"Frequent (79-30%)","criteria":null},{"hpo":"HP:0000083","label":"Renal insufficiency","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0100806","label":"Sepsis","frequency":"Occasional (29-5%)","criteria":null},{"hpo":"HP:0001645","label":"Sudden cardiac death","frequency":"Occasional (29-5%)","criteria":null}]}}