{"orpha":723218,"name":"SITRAME Syndrome","type":"Clinical syndrome","group":"Disorder","status":"active","flags":[],"synonyms":["Systemic inflammatory trunk recurrent acute macular eruption syndrome"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-723218/","orphanet_url":"https://www.orpha.net/en/disease/detail/723218","names":{"fr":{"name":"Syndrome SITRAME","synonyms":["Syndrome inflammatoire systémique prédominant au tronc avec éruption maculaire aigüe récurrente"]},"de":{"name":"SITRAME-Syndrom","synonyms":["Syndrom der systemischen Inflammation mit rezidivierendem akutem makulösem Exanthem des Rumpfes"]},"es":{"name":"Síndrome SITRAME","synonyms":["Síndrome de erupción macular aguda recurrente inflamatoria sistémica en el tronco"]},"it":{"name":"Sindrome SITRAME","synonyms":["Sindrome da eruzione infiammatoria sistemica maculare acuta ricorrente del tronco"]},"nl":{"name":"SITRAME-syndroom","synonyms":["Systemisch inflammatoir syndroom met recidiverende acute maculaire eruptie op romp"]},"pt":{"name":"SITRAME Syndrome"},"pl":{"name":"SITRAME Syndrome","synonyms":["Systemic inflammatory trunk recurrent acute macular eruption syndrome"]},"cs":{"name":"SITRAME Syndrome","synonyms":["Systemic inflammatory trunk recurrent acute macular eruption syndrome"]}},"xrefs":[],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":290842,"name":"Autoinflammatory syndrome with skin involvement","classifications":[187]},{"orpha":324936,"name":"Unclassified autoinflammatory syndrome","classifications":[196]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":47.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"},{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}