{"orpha":715855,"name":"Acute exudative polymorphous vitelliform maculopathy","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["AEPVM"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-715855/","orphanet_url":"https://www.orpha.net/en/disease/detail/715855","names":{"fr":{"name":"Maculopathie vitelliforme polymorphe exsudative aiguë","synonyms":["MVPEA"]},"de":{"name":"Akute exsudative polymorphe vitelliforme Makulopathie","synonyms":["AEPVM"]},"es":{"name":"Maculopatía viteliforme polimorfa exudativa aguda","synonyms":["AEPVM"]},"it":{"name":"Maculopatia vitelliforme polimorfa essudativa acuta","synonyms":["MVPEA"]},"nl":{"name":"Acute exsudatieve polymorfe vitelliforme maculopathie","synonyms":["AEPVM"]},"pt":{"name":"Acute exudative polymorphous vitelliform maculopathy"},"pl":{"name":"Ostra wysiękowa polimorficzna żółtkowata makulopatia","synonyms":["AEPVM"]},"cs":{"name":"Acute exudative polymorphous vitelliform maculopathy","synonyms":["AEPVM"]}},"xrefs":[],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97966,"name":"Rare ophthalmic disorder"},"parents":[{"orpha":716432,"name":"Rare isolated progressive predominantly macular disorder","classifications":[189]}],"children":[{"orpha":715845,"name":"Idiopathic acute exudative polymorphous vitelliform maculopathy","type":"Clinical subtype"},{"orpha":715850,"name":"Paraneoplastic acute exudative polymorphous vitelliform maculopathy","type":"Clinical subtype"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":40.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}