{"orpha":715724,"name":"Diffuse pediatric-type high-grade glioma-H3-wildtype-IDH-wildtype","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-715724/","orphanet_url":"https://www.orpha.net/en/disease/detail/715724","names":{"fr":{"name":"Gliome diffus de haut grade de type pédiatrique IDH-wildtypes et H3-wildtypes"},"de":{"name":"Diffuses hochgradiges Gliom vom pädiatrischen Typ, IDH- und H3-Wildtyp"},"es":{"name":"Glioma difuso de alto grado tipo pediátrico, wildtype-H3 y wildtype-IDH"},"it":{"name":"Glioma diffuso pediatrico di alto grado-H3-tipo selvatico-IDH-tipo selvatico"},"nl":{"name":"Diffuus pediatrisch hooggradig glioom-H3-wildtype-IDH-wildtype"},"pt":{"name":"Diffuse pediatric-type high-grade glioma-H3-wildtype-IDH-wildtype"},"pl":{"name":"Glejak rozlany o wysokim stopniu złośliwości typu dziecięcego-H3-typ dziki-IDH-typ dziki"},"cs":{"name":"Diffuse pediatric-type high-grade glioma-H3-wildtype-IDH-wildtype"}},"xrefs":[{"source":"ICD-10","code":"C71.9","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2A00.0Y","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"XH4Q01","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"150565601"}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":251561,"name":"High-grade astrocytoma","classifications":[181,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adolescent","Childhood"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}