{"orpha":71274,"name":"Disseminated peritoneal leiomyomatosis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["DPL","Diffuse peritoneal leiomyomatosis","LPD","Leiomyomatosis peritonealis disseminate"],"definition":"Disseminated peritoneal leiomyomatosis (DPL) is characterized by the proliferation of multiple benign smooth muscle cell-containing nodules in the peritoneal cavity.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-71274/","orphanet_url":"https://www.orpha.net/en/disease/detail/71274","names":{"fr":{"name":"Léiomyomatose péritonéale disséminée","synonyms":["Léiomyomatose péritonéale diffuse"],"definition":"La léiomyomatose péritonéale disséminée (LPD) se caractérise par la prolifération dans la cavité péritonéale de multiples nodules bénins à cellules musculaires lisses."},"de":{"name":"Peritoneale Leiomyomatose, disseminierte","synonyms":["DPL","LPD","Peritoneale Leiomyomatose, diffuse"],"definition":"Die Disseminierte peritoneale Leiomyomatose (DPL) ist gekennzeichnet durch die Proliferation multipler benigner, glatte Muskelzellen enthaltender Knötchen in der Peritonealhöhle."},"es":{"name":"Leiomiomatosis peritoneal diseminada","synonyms":["LPD","Leiomiomatosis peritoneal difusa"],"definition":"La leiomiomatosis peritoneal diseminada (LPD) se caracteriza por la proliferación en la cavidad peritoneal de múltiples nódulos benignos formados por células musculares lisas."},"it":{"name":"Leiomiomatosi peritoneale disseminata","synonyms":["DPL","LPD","Leiomiomatosi peritoneale diffusa"]},"nl":{"name":"Gedissemineerde peritoneale leiomyomatose","synonyms":["DPL","Diffuse peritoneale leiomyomatose","LPD","Leiomyomatosis peritonealis disseminata"],"definition":"Gedissemineerde peritoneale leiomyomatose (DPL) wordt gekarakteriseerd door proliferatie van multipele, goedaardige knobbeltjes die gladde spiercellen bevatten in de peritoneale holte."},"pt":{"name":"Leiomiomatose peritoneal disseminada","definition":"A leiomiomatose peritoneal disseminada (DPL) é caracterizada pela proliferação de nódulos benignos múltiplos com células musculares lisas na cavidade peritoneal."},"pl":{"name":"Rozsiana zaotrzewnowa leiomiomatoza","synonyms":["Dpl","Leiomyomatosis peritonealis disseminate","LPD","Rozlana zaotrzewnowa leiomiomatoza"]},"cs":{"name":"Diseminovaná peritoneální leiomyomatóza","synonyms":["DPL","Difuzní peritoneální leiomyomatóza","LPD"]},"uk":{"name":"Дисемінований перитонеальний лейоміоматоз","synonyms":["Дифузний перитонеальний лейоміоматоз","DPL","Дисемінований лейоміоматоз очеревини","LPD"],"definition":"Disseminated peritoneal leiomyomatosis (DPL) is characterized by the proliferation of multiple benign smooth muscle cell-containing nodules in the peritoneal cavity."},"zh":{"name":"播散性腹膜平滑肌瘤病","synonyms":["播散性腹膜平滑肌瘤病"]},"tr":{"name":"Yaygın peritoneal leiomiyomatoz","synonyms":["DPL","LPD","Yaygın peritoneal leiomyomatoz","Leiyomyomatozis peritonealis disseminate"]}},"xrefs":[{"source":"ICD-10","code":"D20.1","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2F7C","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"XH8MR2","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"304474672"},{"source":"MONDO","code":"0006183","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0267785","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"12843","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":676030,"name":"Primary benign peritoneal tumor","classifications":[182,202]},{"orpha":506216,"name":"Rare disorder potentially indicated for bowel transplant","classifications":[233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Unknown"],"onset":["Adult"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":150.0,"area":"Worldwide","status":"Validated","source":"[EXPERT]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}