{"orpha":71198,"name":"Rare pulmonary hypertension","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-71198/","orphanet_url":"https://www.orpha.net/en/disease/detail/71198","names":{"fr":{"name":"Hypertension pulmonaire rare"},"de":{"name":"Pulmonale Hypertonie, seltene","synonyms":["Hypertension, pulmonale"]},"es":{"name":"Hipertensión pulmonar rara"},"it":{"name":"Ipertensione polmonare"},"nl":{"name":"Zeldzame pulmonale hypertensie"},"pt":{"name":"Hipertensão pulmonar, rara"},"pl":{"name":"Rzadkie nadciśnienie płucne"},"cs":{"name":"Vzácná plicní hypertenze"},"uk":{"name":"Рідкісна легенева гіпертензія"},"zh":{"name":"罕见肺性高血压"},"tr":{"name":"Nadir pulmoner hipertansiyon"}},"xrefs":[{"source":"MONDO","code":"19096","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5681268","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97955,"name":"Rare respiratory disease"},"parents":[{"orpha":97955,"name":"Rare respiratory disease","classifications":[184]}],"children":[{"orpha":70591,"name":"Chronic thromboembolic pulmonary hypertension","type":"Disease"},{"orpha":182090,"name":"Pulmonary arterial hypertension","type":"Category"},{"orpha":275837,"name":"Pulmonary hypertension owing to lung disease and/or hypoxia","type":"Clinical group"},{"orpha":275844,"name":"Pulmonary hypertension with unclear multifactorial mechanism","type":"Clinical group"},{"orpha":431353,"name":"Pulmonary veno-occlusive disease and/or pulmonary capillary hemangiomatosis","type":"Category"},{"orpha":275853,"name":"Syndrome with pulmonary hypertension as a major feature","type":"Category"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET_25385937[PMID]"}],"phenotypes":null}