{"orpha":698069,"name":"Fibromuscular dysplasia of the arteries of the extremities","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Extremity fibromuscular dysplasia","Fibromuscular dysplasia of the arteries of the limbs","Limb fibromuscular dysplasia"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-698069/","orphanet_url":"https://www.orpha.net/en/disease/detail/698069","names":{"fr":{"name":"Dysplasie fibromusculaire des artères des extrémités"},"de":{"name":"Fibromuskuläre Dysplasie der Arterien der Extremitäten"},"es":{"name":"Displasia fibromuscular de las arterias de las extremidades","synonyms":["Displasia fibromuscular de las arterias de los miembros","Displasia fibromuscular de las extremidades","Displasia fibromuscular de los miembros"]},"it":{"name":"Displasia fibromuscolare delle arterie degli arti","synonyms":["Displasia fibromuscolare delle arterie degli arti","Displasia fibromuscolare degli arti"]},"nl":{"name":"Fibromusculaire dysplasie van arteriën van extremiteiten","synonyms":["Fibromusculaire dysplasie van arteriën van ledematen","Fibromusculaire dysplasie van extremiteiten","Fibromusculaire dysplasie van ledematen"]},"pt":{"name":"Fibromuscular dysplasia of the arteries of the extr"},"pl":{"name":"Fibromuscular dysplasia of the arteries of the extremities","synonyms":["Extremity fibromuscular dysplasia","Fibromuscular dysplasia of the arteries of the limbs","Limb fibromuscular dysplasia"]},"cs":{"name":"Fibromuscular dysplasia of the arteries of the extremities","synonyms":["Extremity fibromuscular dysplasia","Fibromuscular dysplasia of the arteries of the limbs","Limb fibromuscular dysplasia"]}},"xrefs":[{"source":"ICD-10","code":"I77.3","qualifier":"NTBT","icd_relation":"attributed","validated":false},{"source":"ICD-11","code":"BD41.0","qualifier":"NTBT","icd_relation":"attributed","validated":false}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98028,"name":"Rare circulatory system disease"},"parents":[{"orpha":698012,"name":"Fibromuscular dysplasia","classifications":[198]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Value and class","class":"1-9 / 1 000 000","value":1.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}