{"orpha":698036,"name":"Fibromuscular dysplasia of the cervical and intracranial arteries","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Cephalocervical FMD","Cerebrovascular FMD","Cerebrovascular fibromuscular dysplasia"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-698036/","orphanet_url":"https://www.orpha.net/en/disease/detail/698036","names":{"fr":{"name":"Dysplasie fibromusculaire des artères cervicales et intracrâniennes","synonyms":["Dysplasie fibromusculaire de l'artère cervico-crânienne"]},"de":{"name":"Fibromuskuläre Dysplasie der zervikalen und intrakraniellen Arterien","synonyms":["FMD der hirnversorgenden Gefässe","Zerebrovaskuläre FMD","Zerebrovaskuläre fibromuskuläre Dysplasie"]},"es":{"name":"Displasia fibromuscular de las arterias cervicales e intracraneales","synonyms":["DFM cefalocervical","DFM cerebrovascular","Displasia fibromuscular cerebrovascular"]},"it":{"name":"Displasia fibromuscolare delle arterie cervicali e intracraniche","synonyms":["FMD cefalocervicale","FMD cerebrovascolare","Displasia fibromuscolare cerebrovascolare"]},"nl":{"name":"Fibromusculaire dysplasie van cervicale en intracraniële arteriën","synonyms":["Cerebrovasculaire fibromusculaire dysplasie","Cefalocervicale FMD","Cerebrovasculaire FMD"]},"pt":{"name":"Fibromuscular dysplasia of the cervical and intracranial arteries"},"pl":{"name":"Fibromuscular dysplasia of the cervical and intracranial arteries","synonyms":["Cephalocervical FMD","Cerebrovascular FMD","Cerebrovascular fibromuscular dysplasia"]},"cs":{"name":"Fibromuscular dysplasia of the cervical and intracranial arteries","synonyms":["Cephalocervical FMD","Cerebrovascular FMD","Cerebrovascular fibromuscular dysplasia"]}},"xrefs":[{"source":"ICD-10","code":"I77.3","qualifier":"NTBT","icd_relation":"attributed","validated":false},{"source":"ICD-11","code":"BD41.0","qualifier":"NTBT","icd_relation":"index","validated":false,"icd11_uri":"1908137978"}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98028,"name":"Rare circulatory system disease"},"parents":[{"orpha":698012,"name":"Fibromuscular dysplasia","classifications":[198]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}