{"orpha":696830,"name":"Female adnexal tumor of probable Wolffian origin","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["FATWO"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-696830/","orphanet_url":"https://www.orpha.net/en/disease/detail/696830","names":{"fr":{"name":"Tumeur wolffienne annexielle","synonyms":["FATWO"]},"de":{"name":"Wolff'scher-Adnextumor","synonyms":["FATWO","Tumor der weiblichen Adnexe mit vermutlichem Ursprung in den Residuen der Wolff'schen Gänge","Wolff-Adnextumor"]},"es":{"name":"Tumor anexial femenino de probable origen wolffiano","synonyms":["FATWO","TAFOW"]},"it":{"name":"Tumore annessiale femminile di probabile origine wolffiana","synonyms":["FATWO"]},"nl":{"name":"Vrouwelijke tumor van huidadnexen waarschijnlijk ontstaan in gang van Wolff","synonyms":["FATWO"]},"pt":{"name":"Female Adnexal Tumor of Probable Wolffian Origin"},"pl":{"name":"Female adnexal tumor of probable Wolffian origin","synonyms":["FATWO"]},"cs":{"name":"Female adnexal tumor of probable Wolffian origin","synonyms":["FATWO"]}},"xrefs":[{"source":"ICD-10","code":"C57.4","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2C72.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true,"icd11_uri":"null"}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":180220,"name":"Rare uterine adnexal tumor","classifications":[202,205]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult","Elderly"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"},{"type":"Cases/families","qualification":"Case(s)","class":null,"value":90.0,"area":"Worldwide","status":"Validated","source":"30880826[PMID]"}],"phenotypes":null}