{"orpha":685010,"name":"Mesothelioma of the tunica vaginalis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Malignant mesothelioma of the tunica vaginalis"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-685010/","orphanet_url":"https://www.orpha.net/en/disease/detail/685010","names":{"fr":{"name":"Mésothéliome de la tunique vaginale","synonyms":["Mésothéliome malin de la tunique vaginale"]},"de":{"name":"Mesotheliom der Tunica vaginalis","synonyms":["MMTVT","Malignes Mesotheliom der Tunica vaginalis","Malignes Mesotheliom der Tunica vaginalis testis"]},"es":{"name":"Mesotelioma de túnica vaginal","synonyms":["Mesotelioma maligno de la túnica vaginal"]},"it":{"name":"Mesotelioma della tunica vaginale","synonyms":["Mesotelioma maligno della tunica vaginale"]},"nl":{"name":"Mesothelioom van tunica vaginalis","synonyms":["Maligne mesothelioom van tunica vaginalis"]},"pt":{"name":"Mesotelioma da túnica vaginal","synonyms":["Mesotelioma maligno da túnica vaginal"]},"pl":{"name":"Mesothelioma of the tunica vaginalis","synonyms":["Malignant mesothelioma of the tunica vaginalis"]},"cs":{"name":"Mezoteliom tunica vaginalis","synonyms":["Malignant mesothelioma of the tunica vaginalis"]}},"xrefs":[{"source":"ICD-10","code":"C45.7","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2C80.Z","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"975890","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":363472,"name":"Tumor of testis and paratestis","classifications":[185,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Elderly"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":289.0,"area":"Worldwide","status":"Validated","source":"39682143[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"39682143[PMID]_ORPHANET"}],"phenotypes":null}