{"orpha":664787,"name":"Nicolau syndrome","type":"Clinical syndrome","group":"Disorder","status":"active","flags":[],"synonyms":["Embolia cutis medicamentosa","Livedo-like dermatitis"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-664787/","orphanet_url":"https://www.orpha.net/en/disease/detail/664787","names":{"fr":{"name":"Syndrome de Nicolau","synonyms":["Dermite livédoïde de Nicolau","Embolie cutanée médicamenteuse"]},"de":{"name":"Nicolau-Syndrom","synonyms":["Embolia cutis medicamentosa","Livedo-artige Dermatitis"]},"es":{"name":"Síndrome de Nicolau","synonyms":["Dermatitis similar a livedo","Embolia cutis medicamentosa"]},"it":{"name":"Sindrome di Nicolau","synonyms":["Dermatite simil-livedo","Embolia cutis medicamentosa"]},"nl":{"name":"Syndroom van Nicolau","synonyms":["Embolia cutis medicamentosa","Livedo-achtige dermatitis"]},"pt":{"name":"Síndrome Nicolau","synonyms":["Dermatite livedo-like","Embolia cutis medicamentosa"]},"pl":{"name":"Syndrom Nicolaua","synonyms":["Embolia cutis medicamentosa","Livedo-like dermatitis"]},"cs":{"name":"Nicolauův syndrom","synonyms":["Embolia cutis medicamentosa","Livedo-like dermatitis"]},"uk":{"name":"Синдром Ніколау","synonyms":["Медикаментозна емболія шкірного покриву","Ліведоподібний дерматит"]}},"xrefs":[{"source":"ICD-10","code":"T80.1","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0971103","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"971103","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1142083","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10058729","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":90077,"name":"Other acquired skin disease","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":240.0,"area":"Worldwide","status":"Validated","source":"32679363[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"32679363[PMID]_ORPHANET"}],"phenotypes":null}