{"orpha":659744,"name":"Ocular surface squamous neoplasia","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["OSSN"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-659744/","orphanet_url":"https://www.orpha.net/en/disease/detail/659744","names":{"fr":{"name":"Néoplasie squameuse de la surface oculaire","synonyms":["OSSN"]},"de":{"name":"Neoplasie der plattenepithelialen okulären Oberfäche","synonyms":["OSSN","Plattenepitheliale Neoplasie der Bindehaut"]},"es":{"name":"Neoplasia escamosa de la superficie ocular","synonyms":["NESO"]},"it":{"name":"Neoplasia squamosa della superficie oculare","synonyms":["OSSN"]},"nl":{"name":"Squameuze neoplasie van oogoppervlak","synonyms":["OSSN"]},"pt":{"name":"Neoplasia escamosa da superfície ocular","synonyms":["OSSN"]},"pl":{"name":"Neoplazja płaskonabłonkowa powierzchni oka","synonyms":["OSSN"]},"cs":{"name":"Dlaždicobuněčná neoplázie očního povrchu","synonyms":["OSSN"]},"uk":{"name":"Плоскоклітинна неоплазія поверхні ока","synonyms":["OSSN"]}},"xrefs":[{"source":"ICD-10","code":"D48.7","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0971056","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"971056","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4761284","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10082449","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":101950,"name":"Rare eye tumor","classifications":[189,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adolescent","Adult","Childhood","Elderly"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.03,"area":"United States","status":"Validated","source":"23974890[PMID]_ORPHANET"}],"phenotypes":null}