{"orpha":648992,"name":"Non-syndromic bridging bronchus","type":"Morphological anomaly","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-648992/","orphanet_url":"https://www.orpha.net/en/disease/detail/648992","names":{"fr":{"name":"Bridging bronchus non syndromique"},"de":{"name":"Bridging-Bronchus, nicht syndromaler"},"es":{"name":"Bronquio puente no sindrómico"},"it":{"name":"Bronco a cavaliere non sindromico"},"nl":{"name":"Niet-syndromale 'bridging bronchus'"},"pt":{"name":"Brônquio ponte não-sindrómico"},"pl":{"name":"Niesyndromiczna anomalia rozgałęzienia oskrzela"},"cs":{"name":"Nesyndromický přemosťující bronchus"},"uk":{"name":"Несиндромальний перемикаючий бронх"}},"xrefs":[{"source":"ICD-10","code":"Q32.4","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"LA74.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true,"icd11_uri":"null"},{"source":"MONDO","code":"0958267","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"958267","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5816737","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93890,"name":"Rare developmental defect during embryogenesis"},"parents":[{"orpha":649014,"name":"Bronchial malformation","classifications":[147,184,186]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Unknown"],"onset":["Antenatal","Infancy","Neonatal"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":17.0,"area":"Worldwide","status":"Validated","source":"32534300[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"32534300[PMID]_ORPHANET"}],"phenotypes":null}