{"orpha":645350,"name":"Segmental arterial mediolysis","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-645350/","orphanet_url":"https://www.orpha.net/en/disease/detail/645350","names":{"fr":{"name":"Médiolyse artérielle segmentaire"},"de":{"name":"Segmentale arterielle Mediolyse"},"es":{"name":"Mediolisis arterial segmentaria"},"it":{"name":"Mediolisi arteriosa segmentale"},"nl":{"name":"Segmentale arteriële mediolyse"},"pt":{"name":"Mediólise arterial segmentar"},"pl":{"name":"Segmentalna medializa tętnic"},"cs":{"name":"Segmentální arteriální mediolýza"},"uk":{"name":"Сегментарний артеріальний медіоліз"}},"xrefs":[{"source":"ICD-10","code":"I77.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"BD52.0","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1160127418"},{"source":"MONDO","code":"0957452","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4517096","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10086467","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98028,"name":"Rare circulatory system disease"},"parents":[{"orpha":496924,"name":"Non-inflammatory vasculopathy","classifications":[198]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Unknown"],"onset":[],"prevalence":[],"phenotypes":null}