{"orpha":642788,"name":"Cushing syndrome due to cortisol-producing adrenocortical adenoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["CS due to cortisol-producing adrenocortical adenoma"],"definition":"A form of adrenal Cushing syndrome, an endogenous Cushing syndrome (CS), characterized by chronic over-secretion of cortisol due to a benign adrenal tumor that arises from the adrenal cortex.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-642788/","orphanet_url":"https://www.orpha.net/en/disease/detail/642788","names":{"fr":{"name":"Syndrome de Cushing dû à un adénome adrénocortical sécrétant du cortisol","definition":"Forme de syndrome de Cushing surrénalien, un syndrome de Cushing endogène, caractérisé par une hypersécrétion chronique de cortisol due à une tumeur bénigne des surrénales prenant naissance dans le cortex surrénal."},"de":{"name":"Cushing-Syndrom infolge eines Cortisol-produzierenden Nebennierenrinden-Adenoms","synonyms":["CS durch kortisolproduzierendes adrenokortikales Adenom"],"definition":"Eine Form des endogenen Cushing-Syndrom (CS), das durch eine chronische Übersekretion von Cortisol aufgrund eines gutartigen Nebennierentumors gekennzeichnet ist, der von der Nebennierenrinde ausgeht."},"es":{"name":"Síndrome de Cushing por adenoma adrenocortical productor de cortisol","synonyms":["SC por adenoma adrenocortical productor de cortisol"],"definition":"Es una forma del síndrome de Cushing suprarrenal, un síndrome de Cushing (SC) endógeno caracterizado por hipersecreción crónica de cortisol por un tumor suprarrenal benigno con origen en la corteza suprarrenal."},"it":{"name":"Sindrome di Cushing da adenoma adrenocorticale secernente cortisolo","synonyms":["SC da adenoma adrenocorticale secernente cortisolo"]},"nl":{"name":"Syndroom van Cushing door cortisolproducerend adenoom van bijnierschors","synonyms":["CS door cortisolproducerend adrenocorticaal adenoom"],"definition":"Een vorm van adrenaal syndroom van Cushing, een endogeen syndroom van Cushing (CS), gekenmerkt door chronische overmatige secretie van cortisol door een goedaardige adrenale tumor die ontstaat uit bijnierschors."},"pt":{"name":"Síndrome Cushing devido a adenoma adrenocortical produtor de cortisol","synonyms":["SC devido a adenoma adrenocortical produtor de cortisol"],"definition":"Forma da síndrome Cushing adrenal, uma síndrome Cushing endógena (SC), caracterizada pela secreção excessiva crónica de cortisol devido a um tumor adrenal benigno que surge do córtex adrenal."},"pl":{"name":"Zespół Cushinga spowodowany gruczolakiem kory nadnerczy wytwarzającym kortyzol","synonyms":["CS due to cortisol-producing adrenocortical adenoma"]},"cs":{"name":"Cushingův syndrom způsobený adenomem kůry nadledvin produkujícím kortizol","synonyms":["CS due to cortisol-producing adrenocortical adenoma"]},"uk":{"name":"Синдром Кушинга, зумовлений кортизол-продукуючою адренокортикальною аденомою","synonyms":["CS внаслідок кортизолпродукуючої адренокортикальної аденоми"],"definition":"A form of adrenal Cushing syndrome, an endogenous Cushing syndrome (CS), characterized by chronic over-secretion of cortisol due to a benign adrenal tumor that arises from the adrenal cortex."}},"xrefs":[{"source":"ICD-10","code":"E24.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"5A70.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0958258","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"958258","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5816799","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97978,"name":"Rare endocrine disease"},"parents":[{"orpha":647758,"name":"Adrenal Cushing syndrome","classifications":[193]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}