{"orpha":624178,"name":"Non-specific autoimmune supratentorial encephalitis without characteristic antibodies","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Non-specific supratentorial AE without characteristic antibodies"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-624178/","orphanet_url":"https://www.orpha.net/en/disease/detail/624178","names":{"fr":{"name":"Encéphalite auto-immune supratentoriale non-spécifique sans anticorps caractéristiques","synonyms":["EA supratentoriale non-spécifique sans anticorps caractéristiques"]},"de":{"name":"Unspezifische autoimmune supratentorielle Enzephalitis ohne charakteristische Antikörper","synonyms":["Unspezifische supratentorielle AE ohne charakteristische Antikörper"]},"es":{"name":"Encefalitis autoinmune supratentorial inespecífica sin anticuerpos característicos","synonyms":["EA supratentorial inespecífica sin anticuerpos característicos"]},"it":{"name":"Encefalite autoimmune sopratentoriale aspecifica senza anticorpi caratteristici","synonyms":["EA sopratentoriale aspecifica senza anticorpi caratteristici"]},"nl":{"name":"Aspecifieke auto-immune supratentoriële encefalitis zonder typische antilichamen","synonyms":["Aspecifieke supratentoriële AE zonder typische antilichamen"]},"pt":{"name":"Encefalite supratentorial autoimune não-específica sem anticorpos característicos","synonyms":["AE supratentorial não-específica sem anticorpos característicos"]},"pl":{"name":"Nieswoiste autoimmunologiczne nadnamiotowe zapalenie mózgu bez charakterystycznych przeciwciał","synonyms":["Non-specific supratentorial AE without characteristic antibodies"]},"cs":{"name":"Nespecifická autoimunitní supratentoriální encefalitida bez charakteristických protilátek","synonyms":["Non-specific supratentorial AE without characteristic antibodies"]},"uk":{"name":"Неспецифічний аутоімунний супратенторіальний енцефаліт без характерних антитіл","synonyms":["Неспецифічний супратенторіальний АЕ без характерних антитіл"]}},"xrefs":[{"source":"ICD-10","code":"G04.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0850103","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680409","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":622014,"name":"Autoimmune encephalitis","classifications":[181]},{"orpha":166484,"name":"Inflammatory and autoimmune disease with epilepsy","classifications":[181]},{"orpha":36388,"name":"Paraneoplastic neurologic syndrome","classifications":[181]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}