{"orpha":599513,"name":"Acquired factor XIII deficiency","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["aFXIII"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-599513/","orphanet_url":"https://www.orpha.net/en/disease/detail/599513","names":{"fr":{"name":"Déficit acquis en facteur XIII"},"de":{"name":"Faktor XIII-Mangel, erworbener"},"es":{"name":"Deficiencia del factor XIII adquirida"},"it":{"name":"Deficit acquisito del fattore XIII","synonyms":["aFXIII"]},"nl":{"name":"Verworven deficiëntie van factor XIII","synonyms":["aFXIII"]},"pt":{"name":"Deficiência de factor XIII adquirida"},"pl":{"name":"Nabyty niedobór czynnika XIII","synonyms":["aFXIII"]},"cs":{"name":"Získaný deficit faktoru XIII","synonyms":["aFXIII"]},"uk":{"name":"Набутий дефіцит фактора XIII","synonyms":["aFXIII"]}},"xrefs":[{"source":"ICD-10","code":"D68.4","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"3B22","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"939366157"},{"source":"MONDO","code":"0021133","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0238120","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97992,"name":"Rare hematologic disease"},"parents":[{"orpha":166775,"name":"Rare hemorrhagic disorder due to an acquired coagulation factor defect","classifications":[194]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adolescent","Adult","Childhood","Elderly"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":95.0,"area":"Worldwide","status":"Validated","source":"30446212[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"30446212[PMID]_ORPHANET"}],"phenotypes":null}