{"orpha":599495,"name":"Acquired factor VII deficiency","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-599495/","orphanet_url":"https://www.orpha.net/en/disease/detail/599495","names":{"fr":{"name":"Déficit acquis en facteur VII"},"de":{"name":"Faktor VII-Mangel, erworbener"},"es":{"name":"Deficiencia del factor VII adquirida"},"it":{"name":"Deficit acquisito del fattore VII"},"nl":{"name":"Verworven deficiëntie van factor VII"},"pt":{"name":"Deficiência de factor VII adquirida"},"pl":{"name":"Nabyty niedobór czynnika VII"},"cs":{"name":"Získaný deficit faktoru VII"},"uk":{"name":"Набутий дефіцит фактора VII"},"tr":{"name":"Acquired factor VII deficiency"}},"xrefs":[{"source":"ICD-10","code":"D68.4","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"3B2Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1666190962"},{"source":"MONDO","code":"0035738","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4331989","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97992,"name":"Rare hematologic disease"},"parents":[{"orpha":166775,"name":"Rare hemorrhagic disorder due to an acquired coagulation factor defect","classifications":[194]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Cases/families","qualification":"Case(s)","class":null,"value":83.0,"area":"Worldwide","status":"Validated","source":"36546749[PMID]"},{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"36546749[PMID]_ORPHANET"}],"phenotypes":null}