{"orpha":599490,"name":"Acquired factor V deficiency","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-599490/","orphanet_url":"https://www.orpha.net/en/disease/detail/599490","names":{"fr":{"name":"Déficit acquis du facteur V"},"de":{"name":"Faktor V-Mangel, erworbener"},"es":{"name":"Deficiencia del factor V adquirida"},"it":{"name":"Deficit acquisito del fattore V"},"nl":{"name":"Verworven deficiëntie van factor V"},"pt":{"name":"Deficiência de factor V adquirida"},"pl":{"name":"Nabyty niedobór czynnika V"},"cs":{"name":"Získaný deficit faktoru V"},"uk":{"name":"Набутий дефіцит фактора V"}},"xrefs":[{"source":"ICD-10","code":"D68.4","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"3B2Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1671214092"},{"source":"MONDO","code":"0035737","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4329256","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10086006","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97992,"name":"Rare hematologic disease"},"parents":[{"orpha":166775,"name":"Rare hemorrhagic disorder due to an acquired coagulation factor defect","classifications":[194]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult","Elderly"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"<1 / 1 000 000","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"},{"type":"Cases/families","qualification":"Case(s)","class":null,"value":200.0,"area":"Worldwide","status":"Validated","source":"27428013[PMID]_36713339[PMID]_ORPHANET"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.029,"area":"Australia","status":"Validated","source":"15613918[PMID]"},{"type":"Annual incidence","qualification":"Value and class","class":"<1 / 1 000 000","value":0.009,"area":"Singapore","status":"Validated","source":"19404538[PMID]"}],"phenotypes":null}