{"orpha":54272,"name":"Hepatocellular adenoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Hepatocellular adenoma (HA) is a rare benign tumor of the liver.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-54272/","orphanet_url":"https://www.orpha.net/en/disease/detail/54272","names":{"fr":{"name":"Adénome hépatique","definition":"L'adénome hépatocellulaire (AH) est une tumeur bénigne rare du foie."},"de":{"name":"Adenom, hepatozelluläres","definition":"Das Hepatozelluläre Adenom ist ein seltener gutartiger Lebertumor."},"es":{"name":"Adenoma hepatocelular","definition":"El adenoma hepatocelular (HA) es un tumor benigno raro del hígado."},"it":{"name":"Adenoma epatocellulare"},"nl":{"name":"Hepatocellulair adenoom","definition":"Hepatocellulair adenoom (HA) is een zeldzame goedaardige tumor van lever."},"pt":{"name":"Adenoma hepatocelular","definition":"O adenoma hepatocelular (AH) é um tumor benigno raro do fígado."},"pl":{"name":"Gruczolak wątrobowokomórkowy"},"cs":{"name":"Hepatocelulární adenom"},"uk":{"name":"Гепатоцелюлярна аденома","definition":"Hepatocellular adenoma (HA) is a rare benign tumor of the liver."},"zh":{"name":"肝细胞性腺瘤"},"tr":{"name":"Hepatoselüler adenom"}},"xrefs":[{"source":"ICD-10","code":"D13.4","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"2E92.7","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1481070735"},{"source":"ICD-11","code":"XH68V1","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"626046371"},{"source":"MONDO","code":"0018902","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D018248","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0206669","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10019827","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":306636,"name":"Rare tumor of liver and intrahepatic biliary tract","classifications":[183,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult","Elderly"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET_21175790[PMID]"}],"phenotypes":null}