{"orpha":498345,"name":"Biliary atresia and associated disorders","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-498345/","orphanet_url":"https://www.orpha.net/en/disease/detail/498345","names":{"fr":{"name":"Atrésie des voies biliaires et maladies associées"},"de":{"name":"Gallengangatresie und assoziierte Störungen"},"es":{"name":"Atresia biliar y trastornos asociados"},"it":{"name":"Atresia biliare e malattie associate"},"nl":{"name":"Biliaire atresie en geassocieerde aandoeningen"},"pt":{"name":"Atresia biliar e doenças associadas"},"pl":{"name":"Atrezja dróg żółciowych wraz z chorobami towarzyszącymi"},"cs":{"name":"Biliární atrézie a asociované poruchy"},"uk":{"name":"Атрезія жовчовивідних шляхів та повязані з нею розлади"},"zh":{"name":"胆道闭锁及相关疾病"},"tr":{"name":"Biliyer atrezi ve ilişkili bozukluklar"}},"xrefs":[{"source":"UMLS","code":"C5681238","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":57146,"name":"Rare hepatic disease"},"parents":[{"orpha":101941,"name":"Rare biliary tract disease","classifications":[183]}],"children":[{"orpha":30391,"name":"Isolated biliary atresia","type":"Morphological anomaly"},{"orpha":498350,"name":"Syndromic biliary atresia","type":"Clinical group"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}