{"orpha":454821,"name":"OBSOLETE: Pleomorphic salivary gland adenoma","type":"Histopathological subtype","group":"Subtype of disorder","status":"inactive","flags":["Obsolete entity"],"synonyms":[],"definition":null,"note":"This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Benign epithelial tumor of salivary glands","url":"https://raremap.alftech.space/d/ORPHA-454821/","orphanet_url":"https://www.orpha.net/en/disease/detail/454821","names":{"fr":{"name":"OBSOLETE : Adénome pléomorphe de la glande salivaire"},"de":{"name":"OBSOLET: Speicheldrüsenadenom, pleomorphes"},"es":{"name":"OBSOLETO: Adenoma pleomórfico de las glándulas salivales"},"it":{"name":"OBSOLETO: Adenoma pleomorfo delle ghiandole salivari"},"nl":{"name":"OBSOLEET: Pleomorf adenoom van speekselklier","synonyms":["OBSOLEET: Pleiomorf adenoom van speekselklier","OBSOLEET: Pleomorf speekselklieradenoom"]},"pt":{"name":"OBSOLETO: Adenoma pleomórfico da glândula salivar"},"pl":{"name":"NIEAKTUALNE: Pleomorficzny gruczolak ślinianki"},"cs":{"name":"NEAKTUÁLNÍ: Pleomorfní adenom slinných žláz"},"uk":{"name":"Плеоморфна аденома слинної залози","definition":"A rare tumor of salivary glands characterized by a benign, well-circumscribed, slow-growing, painless mass most commonly occurring in the parotid gland (but also the palate, submandibular gland, or nasal septal mucosa), histopathologically composed of epithelial and myoepithelial / stromal components. Possible signs and symptoms depend on the location of the tumor and include facial nerve weakness, mild dysphagia, or unilateral nasal obstruction. Recurrence rates are low, although tumor rupture and spillage have been reported. Malignant transformation may occur in a small percentage of cases."},"zh":{"name":"多形唾液腺腺瘤"},"tr":{"name":"Pleomorfik tükürük bezi adenomu"}},"xrefs":[],"associations":[{"type":"Referred to","orpha":276148,"name":"Benign epithelial tumor of salivary glands"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}