{"orpha":439202,"name":"Non-recovering obstetric brachial plexus lesion","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Chronic obstetric brachial plexus injury","Chronic obstetric brachial plexus palsy","Non-recovering OBPI","Non-recovering OBPL"],"definition":"A rare acquired peripheral neuropathy characterized by paresis of the supraspinatus, infraspinatus, deltoid, and biceps muscles (in C5-C6 injury), wrist and finger extensor muscles (C7 injury), or impaired hand function (C8-Th1 injury) on the affected side due to a traction lesion of the brachial plexus during delivery. The upper trunk of the brachial plexus is most commonly affected, while isolated injury to the lower trunk is very rare. Potential sequelae of brachial plexus injury are muscle atrophy, pain, sensory deficits, and secondary deformities.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-439202/","orphanet_url":"https://www.orpha.net/en/disease/detail/439202","names":{"fr":{"name":"Paralysie obstétricale du plexus brachial sans récupération","synonyms":["POPB sans récupération"],"definition":"Neuropathie périphérique acquise rare caractérisée par une parésie des muscles supra-épineux et infra-épineux, du deltoïde et des biceps (lésions C5-C6), des muscles extenseurs du poignet et des doigts (lésions C7) ou par une fonction réduite de la main (lésions C8-Th1) du côté du corps atteint en raison d'une lésion de traction du plexus brachial pendant l'accouchement. L'atteinte touche le plus souvent le tronc supérieur du plexus brachial, les lésions isolées du tronc inférieur étant très rares. Les éventuelles séquelles des lésions du plexus brachial sont une atrophie musculaire, des douleurs, des déficits sensoriels et des malformations secondaires."},"de":{"name":"Geburtstraumatische Läsion des Plexus brachialis, nicht-heilende","synonyms":["Armplexusparese, chronische geburtstraumatische","Chronische geburtstraumatische Armplexusverletzung","OBPI, nicht-heilend","OBPL, nicht-heilend"],"definition":"Eine seltene erworbene periphere Neuropathie mit Paresen des M. supraspinatus, M. infraspinatus, M. deltoideus und M. biceps (bei Läsion C5-C6), der Handgelenks- und Fingerstreckmuskulatur (Läsion C7) oder einer eingeschränkten Handfunktion (Läsion C8-Th1) auf der betroffenen Seite als Folge einer Zugläsion des Plexus brachialis während der Geburt. Am häufigsten ist der obere Teil des Plexus brachialis betroffen, während eine isolierte Schädigung des unteren Teils sehr selten ist. Mögliche Folgen einer Verletzung des Plexus brachialis sind Muskelschwund, Schmerzen, sensorische Defizite und sekundäre Deformitäten."},"es":{"name":"Lesión del plexo braquial obstétrica sin recuperación","synonyms":["Lesión del plexo braquial obstétrica crónica","OBPI sin recuperación","OBPL sin recuperación"],"definition":"Es una neuropatía periférica adquirida poco frecuente caracterizada por paresia de los músculos supraespinoso, infraespinoso, deltoides y bíceps (lesión C5-C6), de los músculos extensores de la muñeca y los dedos (lesión C7) o alteración de la función de la mano (lesión C8-T1) en el lado afectado debido a una lesión por tracción del plexo braquial durante el parto. El tronco superior del plexo braquial se ve afectado con mayor frecuencia, mientras que las lesiones aisladas de la parte inferior del tronco son muy infrecuentes. Las posibles secuelas de la lesión del plexo braquial son atrofia muscular, dolor, déficits sensitivos y deformidades secundarias."},"it":{"name":"Lesione ostetrica del plesso brachiale non remittente","synonyms":["Lesione ostetrica cronica del plesso brachiale","OBPI non remittente","OBPL non remittente","Paralisi ostetrica cronica del plesso brachiale"],"definition":"Si tratta di una neuropatia periferica acquisita rara, caratterizzata dalla paresi dei muscoli sovraspinato, infraspinato, deltoide e bicipite (lesione C5-C6), dei muscoli estensori del polso e delle dita della mano (lesione C7) o dalla compromissione della funzione della mano (lesione C8-Th1) del lato interessato, secondarie ad una lesione da trazione del plesso brachiale durante il parto. Sono più comuni le lesioni del tronco superiore del plesso brachiale, mentre quelle isolate del tronco inferiore sono molto rare. Le potenziali sequele della lesione del plesso brachiale sono l'atrofia muscolare, il dolore, i deficit sensoriali e le deformità secondarie."},"nl":{"name":"Niet-herstellende obstetrische plexus brachialis-laesie","synonyms":["Chronisch obstetrisch plexus brachialis-letsel","Chronische obstetrische plexus brachialis-verlamming","Niet-herstellend OBPI","Niet-herstellend OBPL"],"definition":"Een zeldzame, verworven perifere neuropathie, gekarakteriseerd door parese van musculus supraspinatus, infraspinatus, deltoideus, en biceps (bij C5-C6 letsel), strekspieren van pols en vinger (C7 letsel), of verstoorde handfunctie (C8-Th1 letsel) aan de getroffen zijde als gevolg van een tractieletsel van plexus brachialis tijdens de bevalling. In de meeste gevallen wordt de bovenste wortel van de plexus brachialis getroffen, terwijl geïsoleerd letsel van de onderste wortel zeer zeldzaam is. Potentiële restverschijnselen van letsel van plexus brachialis zijn spieratrofie, pijn, sensorische stoornissen, en secundaire misvorming."},"pt":{"name":"Lesão obstétrica do plexo braquial, sem recuperação"},"pl":{"name":"Niegojące się okołoporodowe uszkodzenie splotu ramiennego","synonyms":["Niegojący OBpl","Niegojący się OBPI","Przewlekłe okołoporodowe porażenie splotu ramiennego","Przewlekłe okołoporodowe uszkodzenie splotu ramiennego"]},"cs":{"name":"Nehojící se poporodní léze brachiálního plexu","synonyms":["Chronické poporodní ochrnutí brachiálního plexu","Nehojící se OBPI","Nehojící se OBPL","Chronické poporodní poranění brachiálního plexu"]},"uk":{"name":"Невідновлюване акушерське ураження плечового сплетіння","synonyms":["Хронічна акушерська травма плечового сплетення","Хронічний акушерський параліч плечового сплетіння","Невідновлювані OBPI","Безнадійні кредити, що не підлягають поверненню"],"definition":"A rare acquired peripheral neuropathy characterized by paresis of the supraspinatus, infraspinatus, deltoid, and biceps muscles (in C5-C6 injury), wrist and finger extensor muscles (C7 injury), or impaired hand function (C8-Th1 injury) on the affected side due to a traction lesion of the brachial plexus during delivery. The upper trunk of the brachial plexus is most commonly affected, while isolated injury to the lower trunk is very rare. Potential sequelae of brachial plexus injury are muscle atrophy, pain, sensory deficits, and secondary deformities."},"zh":{"name":"不可逆性产科臂丛神经病变","synonyms":["慢性产科臂丛神经损伤"],"definition":"一种罕见的获得性周围神经病，其特征是冈上肌、冈下肌、三角肌和二头肌轻瘫（C5-C6损伤），腕部和手指伸肌（C7损伤）或手功能受损（C8-Th1损伤）。可由分娩过程中臂丛神经的牵引导致病变。臂丛神经的上束最常受累，而下束的孤立损伤非常少见。臂丛神经损伤的潜在后遗症包括肌肉萎缩，疼痛，感觉缺失和继发畸形。"},"tr":{"name":"İyileşmeyen obstetrik brakiyal pleksus lezyonu","synonyms":["İyileşmeyen OBPI","İyileşmeyen OBPL","Kronik obstetrik brakiyal pleksus felci","Kronik obstetrik brakiyal pleksus yaralanması"]}},"xrefs":[{"source":"ICD-10","code":"P14.3","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0018587","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680048","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":182086,"name":"Acquired peripheral neuropathy","classifications":[181]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}