{"orpha":399302,"name":"Primary avascular necrosis","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["Primary AVN"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-399302/","orphanet_url":"https://www.orpha.net/en/disease/detail/399302","names":{"fr":{"name":"Nécrose avasculaire primaire","synonyms":["AVN primaire"]},"de":{"name":"Avaskuläre Nekrose, primäre","synonyms":["Primäre AVN"]},"es":{"name":"Necrosis avascular primaria","synonyms":["AVN primaria"]},"it":{"name":"Necrosi avascolare primitiva","synonyms":["AVN primitiva"]},"nl":{"name":"Primaire avasculaire necrose","synonyms":["Primaire AVN"]},"pt":{"name":"Necrose avascular primária"},"pl":{"name":"Pierwotna martwica awaskularna","synonyms":["Pierwotna AVN"]},"cs":{"name":"Primární avaskulární nekróza","synonyms":["Primární AVN"]},"uk":{"name":"Первинний аваскулярний некроз","synonyms":["Первинний AVN"]},"zh":{"name":"原发性缺血性坏死","synonyms":["原发性AVN"]},"tr":{"name":"Primer avasküler nekroz","synonyms":["Primer AVN"]}},"xrefs":[{"source":"MONDO","code":"0018379","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"18379","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680038","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":93419,"name":"Rare bone disease"},"parents":[{"orpha":399164,"name":"Avascular necrosis","classifications":[196,199]}],"children":[{"orpha":86820,"name":"Familial avascular necrosis of femoral head","type":"Disease"},{"orpha":399307,"name":"Idiopathic avascular necrosis","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}