{"orpha":398940,"name":"Malignant non-epithelial tumor of ovary","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":["Non-epithelial cancer of ovary","Ovarian malignant non-epithelial tumor","Ovarian non-epithelial cancer"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-398940/","orphanet_url":"https://www.orpha.net/en/disease/detail/398940","names":{"fr":{"name":"Tumeur non épithéliale maligne de l'ovaire","synonyms":["Cancer non épithélial de l'ovaire","Tumeur ovarienne non épithéliale maligne"]},"de":{"name":"Maligner nicht-epithelialer Tumor des Ovars","synonyms":["Nicht-epithelialer Eierstockkrebs","Ovarialkarzinom, non-epitheliales"]},"es":{"name":"Tumor no epitelial maligno de ovario","synonyms":["Cáncer no epitelial de ovario","Cáncer ovárico no epitelial","Tumor ovárico no epitelial maligno"]},"it":{"name":"Tumore non epiteliale maligno dell'ovaio","synonyms":["Cancro non epiteliale dell'ovaio","Cancro non epiteliale ovarico","Tumore non epiteliale ovarico maligno"]},"nl":{"name":"Maligne niet-epitheliale tumor van ovarium","synonyms":["Kwaadaardige niet-epitheliale ovariumtumor","Niet-epitheliale eierstokkanker","Ovariële niet-epitheliale kanker"]},"pt":{"name":"Tumor não epitelial maligno do ovário"},"pl":{"name":"Nienabłonkowy złośliwy guz jajnika","synonyms":["Nienabłonkowy rak jajnika","Nienabłonkowy rak jajnika","Nienabłonkowy złośliwy guz jajnika"]},"cs":{"name":"Maligní neepiteliální nádory ovaria","synonyms":["Ovariální maligní non-epiteliální nádor","Ovariální neepiteliální zhoubné nádory","Neepiteliální zhoubné nádory vaječníku"]},"uk":{"name":"Злоякісна неепітеліальна пухлина яєчника","synonyms":["Неепітеліальний рак яєчника","Злоякісна неепітеліальна пухлина яєчника","Неепітеліальний рак яєчників"]},"zh":{"name":"恶性卵巢非上皮性肿瘤","synonyms":["卵巢恶性非上皮性肿瘤"]},"tr":{"name":"Overin epitelyal olmayan habis tümörü","synonyms":["Epitel dışı over kanseri","Epitel dışı over kanseri","Habis over epitel dışı tümörü"]}},"xrefs":[{"source":"MONDO","code":"0018365","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"18365","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680039","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[{"type":"Referred to","orpha":213517,"name":"OBSOLETE: Familial ovarian cancer","status":"inactive"}],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":213500,"name":"Rare ovarian cancer","classifications":[202,205]}],"children":[{"orpha":206484,"name":"Gonadoblastoma","type":"Disease"},{"orpha":35807,"name":"Malignant germ cell tumor of ovary","type":"Category"},{"orpha":35808,"name":"Malignant sex cord stromal tumor of ovary","type":"Category"},{"orpha":398987,"name":"Malignant teratoma of ovary","type":"Disease"},{"orpha":370396,"name":"Small cell carcinoma of the ovary","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Annual incidence","qualification":"Value and class","class":"1-9 / 1 000 000","value":0.43,"area":"Europe","status":"Validated","source":"RARECARE surveillance of rare cancers in Europe[OTHER]"}],"phenotypes":null}