{"orpha":363567,"name":"Acute encephalopathy with inflammation-mediated status epilepticus","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-363567/","orphanet_url":"https://www.orpha.net/en/disease/detail/363567","names":{"fr":{"name":"Encéphalopathie épileptique aiguë fébrile","synonyms":["AEIMSE"]},"de":{"name":"Akute Enzephalopathie mit entzündungsvermitteltem Status Epilepticus"},"es":{"name":"Encefalopatía aguda con estado epiléptico mediado por una inflamación"},"it":{"name":"Encefalopatia acuta con stato epilettico mediato da un'infiammazione"},"nl":{"name":"Acute encefalopathie met inflammatiegemedieerde status epilepticus"},"pt":{"name":"Encefalopatia aguda com estado epiléptico mediado por inflamação"},"pl":{"name":"Ostra encefalopatia ze stanem padaczkowym wywołana stanem zapalnym"},"cs":{"name":"Akutní encefalopatie se status epilepticus na podkladě zánětu"},"uk":{"name":"Гостра енцефалопатія з епілептичним статусом, повязана з запаленням"},"zh":{"name":"急性脑病伴炎症介导的癫痫持续状态"},"tr":{"name":"İnflamasyon aracılı status epileptikus ile seyreden akut ensefalopati"}},"xrefs":[{"source":"MONDO","code":"18200","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5680984","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":98259,"name":"Childhood-onset epilepsy syndrome","classifications":[181]},{"orpha":166484,"name":"Inflammatory and autoimmune disease with epilepsy","classifications":[181]}],"children":[{"orpha":363549,"name":"Acute encephalopathy with biphasic seizures and late reduced diffusion","type":"Disease"},{"orpha":163703,"name":"Febrile infection-related epilepsy syndrome","type":"Disease"},{"orpha":363558,"name":"New-onset refractory status epilepticus","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}