{"orpha":36273,"name":"Gastric linitis plastica","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":["Borrmann gastric cancer type 4","Linitis plastica of the stomach"],"definition":"Gastric linitis plastica (gastric LP) is a malignant, diffuse, infiltrative gastric adenocarcinoma.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-36273/","orphanet_url":"https://www.orpha.net/en/disease/detail/36273","names":{"fr":{"name":"Linite gastrique","synonyms":["Cancer de l'estomac type Borrmann 4","Linite plastique de l'estomac"],"definition":"La linite gastrique (LG) est un adénocarcinome gastrique malin, diffus et infiltrant."},"de":{"name":"Gastrische Linitis plastica","synonyms":["Linitis plastica des Magens","Magenkrebs, Typ Borrmann 4"],"definition":"Die Gastrische Linitis plastica (GLP) ist ein malignes, diffuses, infiltratives Adenokarzinom des Magens."},"es":{"name":"Linitis plástica gástrica","definition":"La linitis plástica gástrica (LP gástrica) es un adenocarcinoma gástrico infiltrante, difuso y maligno."},"it":{"name":"Linite plastica","synonyms":["Cancro dello stomaco, tipo Bormann 4","Linite plastica dello stomaco"]},"nl":{"name":"Linitis plastica van maag","synonyms":["Borrmann-maagkanker type 4"],"definition":"Een maligne, diffuus, infiltratief adenocarcinoom van maag."},"pt":{"name":"Linhite plástica","synonyms":["Cancro gástrico tipo Borrmann 4","Linhite plástica do estômago"],"definition":"A linhite plástica gástrica (LP gástrica) é um adenocarcinoma gástrico infiltrativo, difuso e maligno. A LP gástrica representa cerca de 10% de todos os cancros gástricos, mas a prevalência exata na população geral é desconhecida."},"pl":{"name":"Rozlany typ raka żołądka","synonyms":["Rak rozlany żołądka","Rak żołądka Borrmanna typu 4"]},"cs":{"name":"Linitis plastica","synonyms":["Linitis plastica žaludku","Borrmannův karcinom žaludku, typ 4"]},"uk":{"name":"Пластичний лініт шлунка","synonyms":["Рак шлунка Боррманна, тип 4","Пластичний лініт шлунка"],"definition":"Gastric linitis plastica (gastric LP) is a malignant, diffuse, infiltrative gastric adenocarcinoma."},"zh":{"name":"皮革胃","synonyms":["皮革胃"]},"tr":{"name":"Mide linitis plastika","synonyms":["Borrmann mide kanseri tip 4","Midenin Linitis plastica"]}},"xrefs":[{"source":"ICD-10","code":"C16.9","qualifier":"NTBT","icd_relation":"index","validated":true},{"source":"ICD-11","code":"2B72.0","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1165754036"},{"source":"MONDO","code":"0018184","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C4303226","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":423771,"name":"Rare carcinoma of stomach","classifications":[152,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}