{"orpha":36204,"name":"Intestinal lymphangiectasia","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-36204/","orphanet_url":"https://www.orpha.net/en/disease/detail/36204","names":{"fr":{"name":"Lymphangiectasie intestinale"},"de":{"name":"Lymphangiektasie, intestinale"},"es":{"name":"Linfangiectasia intestinal"},"it":{"name":"Linfangectasia intestinale"},"nl":{"name":"Intestinale lymfangiëctasie"},"pt":{"name":"Linfangiectasia intestinal"},"pl":{"name":"Limfangiektazja jelitowa"},"cs":{"name":"Střevní lymfangiektázie"},"uk":{"name":"Кишкова лімфангіектазія"},"zh":{"name":"肠淋巴管扩张"},"tr":{"name":"Bağırsak lenfanjiektazi"}},"xrefs":[{"source":"ICD-11","code":"BD92.0","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"1255239964"},{"source":"MONDO","code":"0018178","qualifier":"E","icd_relation":null,"validated":true},{"source":"MONDO","code":"18178","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D008201","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0024215","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"12331","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10025213","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97935,"name":"Rare gastroenterologic disease"},"parents":[{"orpha":117569,"name":"Rare intestinal disease","classifications":[152]}],"children":[{"orpha":566175,"name":"Complement hyperactivation-angiopathic thrombosis-protein-losing enteropathy syndrome","type":"Disease"},{"orpha":90362,"name":"Primary intestinal lymphangiectasia","type":"Disease"},{"orpha":90363,"name":"Secondary intestinal lymphangiectasia","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}