{"orpha":357131,"name":"Venous thoracic outlet syndrome","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["Venous scalenus anticus syndrome","Venous thoracic outlet compression syndrome","Effort subclavian vein thrombosis","Paget-Schrotter disease","VTOS","Venous TOS","Venous cervical rib syndrome","Venous costoclavicular syndrome","Venous hyperabduction syndrome"],"definition":"Venous thoracic outlet syndrome (VTOS) is a form of thoracic outlet syndrome (TOS) that manifests as unilateral (rarely bilateral) arm pain and cyanosis.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-357131/","orphanet_url":"https://www.orpha.net/en/disease/detail/357131","names":{"fr":{"name":"Syndrome veineux du défilé thoracique","synonyms":["Maladie de Paget-Schrotter","SDT veineux","Syndrome veineux d'hyperabduction","Syndrome veineux de la côte cervicale","Syndrome veineux de la traversée cervico-thoraco-brachiale","Syndrome veineux du défilé cervico-thoraco-brachial","Syndrome veineux du défilé costo-claviculaire","Syndrome veineux du scalène antérieur","TOS veineux","Thrombose d'effort de la veine sous-clavière","VTOS"],"definition":"Le syndrome veineux du défilé thoracique (SDT veineux) est une forme de syndrome du défilé thoracique (SDT) qui se manifeste par une douleur unilatérale (rarement bilatérale) au niveau des bras et une cyanose."},"de":{"name":"Thoracic-outlet-Syndrom, venöses","synonyms":["Effort-Subclaviathrombose","Halsrippensyndrom, venöses","Hyperabduktionssyndrom, venöses","Kostoklavikularsyndrom, venöses","Paget-Schrotter-Krankheit","Paget-von-Schroetter-Syndrom","Scalenus-anticus-Syndrom, venöses","VTOS","Venöses TOS","Venöses Thoracic-outlet-Kompressions-Syndrom"],"definition":"Das venöse Thoracic-outlet-Syndrom (VTOS) ist eine Form des Thoracic-outlet-Syndroms (TOS; siehe dort), das mit einseitigen (selten beidseitigen) Schmerzen und Zyanose der Arme manifest wird."},"es":{"name":"Síndrome venoso de la salida torácica","synonyms":["Enfermedad de Paget-Schrotter","Síndrome venoso costoclavicular","Síndrome venoso de compresión de la salida torácica","Síndrome venoso de hiperabducción","Síndrome venoso de la costilla cervical","Síndrome venoso del escaleno anterior","TOS venoso","Trombosis de esfuerzo de la vena subclavia","VTOS"],"definition":"El síndrome venoso de la salida torácica (VTOS) es una forma del síndrome de salida torácica (TOS; consulte este término) que manifiesta dolor unilateral (raramente bilateral) en un brazo y cianosis."},"it":{"name":"Sindrome venosa dello stretto toracico superiore","synonyms":["Malattia di Paget-Schrotter","Sindrome costoclavicolare venosa","Sindrome venosa compressiva dello stretto toracico superiore","Sindrome venosa da iperabduzione","Sindrome venosa della costa cervicale","Sindrome venosa dello scaleno antico","TOS venosa","Trombosi da sforzo della vena succlavia","VTOS"],"definition":"La sindrome venosa dello stretto toracico (VTOS) è una forma della sindrome dello stretto toracico (TOS; si veda questo termine), che si manifesta con dolore monolaterale (raramente bilaterale) e cianosi del braccio."},"nl":{"name":"Veneus thoracic outlet-syndroom","synonyms":["Veneuze cervicale rib-syndroom","Veneuze hyperabductie-syndroom","Trombose van ondersleutelbeenader door inspanning","Trombose van vena subclavia door inspanning","VTOS","Veneus TOS","Veneus costoclaviculair syndroom","Veneus scalenus anticus-syndroom","Veneus thoracic outlet compressiesyndroom"],"definition":"Veneus thoracic outlet-syndroom (VTOS) is een vorm van thoracic outlet-syndroom (TOS; zie deze term) die zich manifesteert met unilaterale (zelden bilaterale) pijn en cyanose aan de arm."},"pt":{"name":"Síndrome do trato de saída venoso torácico"},"pl":{"name":"Żylny zespół górnego otworu klatki piersiowej","synonyms":["Choroba Pageta i Schrottera","VTOS","Wysiłkowa zakrzepica żyły podobojczykowej","Żylny TOS","Żylny zespół mięśni pochyłych","Żylny zespół nadmiernego odwiedzenia","Żylny zespół ucisku górnego otworu klatki piersiowej","Żylny zespół żebra szyjnego","Żylny zespół żebrowo-obojczykowy"]},"cs":{"name":"Venózní syndrom horní hrudní apertury","synonyms":["VTOS","Venózní TOS","Venózní kostoklavikulární syndrom","Venózní scalenus anticus syndrom","Venózní syndrom horní hrudní apertury, kompresivní","Ponámahová trombóza podklíčkové žíly","Pagetův-Schroetterův syndrom","Venózní syndrom krčního žebra","Venózní hyperabdukční syndrom","Paget-Schroetterův syndrom"]},"uk":{"name":"Синдром венозного грудного виходу","synonyms":["Тромбоз підключичної вени","Хвороба Педжета-Шроттера","Венозний шийно-реберний синдром","Венозний костоклавікулярний синдром","Синдром венозної гіперабдукції","Синдром венозного скаленус-антикуса","Синдром стиснення венозного грудного виходу","Венозний TOS","VTOS"],"definition":"Venous thoracic outlet syndrome (VTOS) is a form of thoracic outlet syndrome (TOS; see this term) that manifests as unilateral (rarely bilateral) arm pain and cyanosis."},"zh":{"name":"静脉胸廓出口综合征","synonyms":["静脉胸廓出口压迫综合征"],"definition":"静脉胸廓出口综合征(VTOS)是胸廓出口综合征(TOS)的一种形式，表现为单侧(双侧罕见)手臂疼痛和发紫。"},"tr":{"name":"Venöz torasik çıkış sendromu","synonyms":["VTOS","Venöz TOS","Paget-Schroetter hastalığı","Venöz servikal kaburga sendromu","Venöz hiperabdüksiyon sendromu","Venöz kostoklaviküler sendrom","Venöz skalen antikus sendromu","Efor subklavyen ven trombozu","Venöz torasik çıkış kompresyon sendromu"]}},"xrefs":[{"source":"ICD-10","code":"G54.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"8B91.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true,"icd11_uri":"null"},{"source":"MONDO","code":"0018165","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1956396","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97962,"name":"Rare surgical thoracic disease"},"parents":[{"orpha":97330,"name":"Thoracic outlet syndrome","classifications":[186]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}