{"orpha":357107,"name":"Arterial thoracic outlet syndrome","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["ATOS","Arterial TOS","Arterial cervical rib syndrome","Arterial costoclavicular syndrome","Arterial hyperabduction syndrome","Arterial scalenus anticus syndrome","Arterial thoracic outlet compression syndrome"],"definition":"A form of thoracic outlet syndrome that presents as unilateral upper extremity ischemia.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-357107/","orphanet_url":"https://www.orpha.net/en/disease/detail/357107","names":{"fr":{"name":"Syndrome artériel du défilé thoracique","synonyms":["Syndrome artériel du défilé cervico-thoraco-brachial","Syndrome artériel du défilé costo-claviculaire","Syndrome artériel du scalène antérieur","TOS artériel","ATOS","SDT artériel","Syndrome artériel d'hyperabduction","Syndrome artériel de la côte cervicale","Syndrome artériel de la traversée cervico-thoraco-brachiale"],"definition":"Le syndrome artériel du défilé thoracique (SDT artériel) est une forme de syndrome du défilé thoracique (SDT) qui se présente par une ischémie unilatérale des membres supérieurs."},"de":{"name":"Thoracic-outlet-Syndrom, arterielles","synonyms":["ATOS","Arterielles TOS","Arterielles Thoracic-outlet-Kompressions-Syndrom","Halsrippensyndrom, arterielles","Hyperabduktionssyndrom, arterielles","Kostoklavikularsyndrom, arterielles","Scalenus-anticus-Syndrom, arterielles"],"definition":"Das arterielle Thoracic-outlet-Syndrom (ATOS) ist eine Form des Thoracic-outlet-Syndroms (TOS; siehe dort), dass sich mit einseitiger Ischämie der oberen Extremitäten manifestiert."},"es":{"name":"Síndrome arterial de la salida torácica","synonyms":["ATOS","Síndrome arterial de compresión de la salida torácica","Síndrome arterial de hiperabducción","Síndrome arterial de la costilla cervical","Síndrome arterial del escaleno anterior","Síndrome costoclavicular arterial","TOS arterial"],"definition":"Es una forma del síndrome de salida torácica que cursa con una isquemia unilateral de las extremidades superiores."},"it":{"name":"Sindrome arteriosa dello stretto toracico superiore","synonyms":["ATOS","Sindrome arteriosa compressiva dello stretto toracico superiore","Sindrome arteriosa da iperabduzione","Sindrome arteriosa della costa cervicale","Sindrome arteriosa dello scaleno antico","Sindrome costoclavicolare arteriosa","TOS arteriosa"],"definition":"La sindrome arteriosa dello stretto toracico (ATOS) è una forma della sindrome dello stretto toracico (TOS; si veda questo termine), che si presenta con ischemia monolaterale agli arti superiori."},"nl":{"name":"Arterieel thoracic outlet-syndroom","synonyms":["ATOS","Arterieel TOS","Arterieel cervicale rib-syndroom","Arterieel costoclaviculair syndroom","Arterieel hyperabductiesyndroom","Arterieel scalenus anticus-syndroom","Arterieel schoudergordelsyndroom","Arterieel thoracic outlet compressiesyndroom"],"definition":"Een vorm van thoracic outletsyndroom die voorkomt als unilaterale ischemie van bovenste ledematen."},"pt":{"name":"Síndrome do desfiladeiro torácico arterial"},"pl":{"name":"Tętniczy zespół górnego otworu klatki piersiowej","synonyms":["ATOS","Tętniczy TOS","Tętniczy zespół mięśni pochyłych","Tętniczy zespół nadmiernego odwiedzenia","Tętniczy zespół ucisku górnego otworu klatki piersiowej","Tętniczy zespół żebra szyjnego","Tętniczy zespół żebrowo-obojczykowy"]},"cs":{"name":"Arteriální syndrom horní hrudní apertury","synonyms":["ATOS","Arteriální TOS","Arteriální kostoklavikulární syndrom","Arteriální syndrom horní hrudní apertury, kompresivní","Arteriální syndrom krčního žebra","Arteriální hyperabdukční syndrom"]},"uk":{"name":"Синдром артеріального виходу з грудної клітки","synonyms":["Артеріальний шийно-реберний синдром","Артеріальний костоключичний синдром","Синдром артеріальної гіперабдукції","Синдром артеріального червоного плескатого лишаю","Синдром здавлення артеріального виходу грудної клітки","Артеріальний TOS","ATOS"],"definition":"A form of thoracic outlet syndrome that presents as unilateral upper extremity ischemia."},"zh":{"name":"动脉胸廓出口综合征","synonyms":["动脉胸廓出口压迫综合征"],"definition":"胸廓出口综合征的一种形式，表现为单侧上肢缺血。"},"tr":{"name":"Arteriyel torasik çıkış sendromu","synonyms":["ATOS","Arteriyel TOS","Arteriyel servikal kaburga sendromu","Arteriyel hiperabdüksiyon sendromu","Arteriyel kostoklaviküler sendrom","Arteriyel skalen antikus sendromu","Arteriyel torasik çıkış kompresyon sendromu"]}},"xrefs":[{"source":"ICD-10","code":"G54.0","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"8B91.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true,"icd11_uri":"null"},{"source":"MONDO","code":"0018164","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C1956395","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97962,"name":"Rare surgical thoracic disease"},"parents":[{"orpha":97330,"name":"Thoracic outlet syndrome","classifications":[186]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":[],"prevalence":[],"phenotypes":null}