{"orpha":345,"name":"Dissecting cellulitis of the scalp","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"Dissecting cellulitis of the scalp is a rare chronic suppurative dermatosis of the scalp that mainly affects black men and that is characterized by multiple painful inflammatory follicular and perifollicular nodules, pustules, and abscesses that interconnect via sinus tracts and eventually result in scarring alopecia.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-345/","orphanet_url":"https://www.orpha.net/en/disease/detail/345","names":{"fr":{"name":"Folliculite disséquante du cuir chevelu","synonyms":["Cellulite disséquante du cuir chevelu"],"definition":"La folliculite disséquante du cuir chevelu est une dermatose suppurative chronique et rare du cuir chevelu affectant principalement les hommes noirs. Elle se manifeste par de nombreux nodules inflammatoires folliculaires et périfolliculaires douloureux, des pustules et des abcès qui s'interconnectent via des tractus sinusaux, ce qui aboutit finalement à une alopécie cicatricielle."},"de":{"name":"Dissezierende Zellulitis der Kopfhaut","synonyms":["Perifolliculitis capitis abscedens et suffodiens"],"definition":"Die Dissezierende Zellulitis der Kopfhaut ist eine seltene, eitrige Dermatose der Kopfhaut, von der vor allem Männer schwarzer Hautfarbe betroffen sind. Charakteristisch sind multiple schmerzhafte entzündliche follikuläre und perifollikulärem Knötchen, Pusteln und Abszesse, die miteinander verbunden sind und eventuell zu narbiger Alopezie führen."},"es":{"name":"Foliculitis disecante de cuero cabelludo","synonyms":["Celulitis disecante de cuero cabelludo"],"definition":"La foliculitis disecante de cuero cabelludo es una dermatosis supurativa crónica rara del cuero cabelludo que afecta principalmente a hombres negros y que se caracteriza por múltiples nódulos foliculares y perifoliculares inflamatorios dolorosos, pústulas, y abscesos que se interconectan a través de fístulas y que finalmente dan lugar a una alopecia cicatricial."},"it":{"name":"Follicolite dissecante del cuoio capelluto","synonyms":["Cellulite disseccante del cuoio capelluto"],"definition":"La cellulite dissecante del cuoio capelluto è una dermatosi suppurativa cronica rara del cuoio capelluto, che interessa soprattutto i maschi di colore, che è caratterizzata da noduli perifollicolari e follicolari infiammatori dolorosi multipli, pustole e ascessi che si interconnettono attraverso i tratti sinusali, provocando l'alopecia cicatriziale."},"nl":{"name":"Dissecerende cellulitis van hoofdhuid","synonyms":["Perifolliculitis capitis abscedens et suffodiens"],"definition":"Dissecerende cellulitis van hoofdhuid is een zeldzame chronische suppuratieve dermatose van scalp, die vooral zwarte mannen treft, en gekenmerkt wordt door multipele pijnlijke inflammatoire folliculaire en perifolliculaire noduli, pustels, en abcessen die met elkaar verbonden zijn via fistels en uiteindelijk resulteren in cicatriciële alopecie."},"pt":{"name":"Celulite dissecante do couro cabeludo"},"pl":{"name":"Rozwarstwiające zapalenie mieszków włosowych"},"cs":{"name":"Disekující celulitida skalpu"},"uk":{"name":"Розсікаючий целюліт волосистої частини голови","definition":"Dissecting cellulitis of the scalp is a rare chronic suppurative dermatosis of the scalp that mainly affects black men and that is characterized by multiple painful inflammatory follicular and perifollicular nodules, pustules, and abscesses that interconnect via sinus tracts and eventually result in scarring alopecia."},"zh":{"name":"头皮切割性蜂窝组织炎"},"tr":{"name":"Kafa derisinin diseksiyonu selüliti"}},"xrefs":[{"source":"OMIM","code":"260910","qualifier":"E","icd_relation":null,"validated":true},{"source":"ICD-10","code":"L66.3","qualifier":"E","icd_relation":"specific","validated":true},{"source":"ICD-11","code":"ED70.51","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"872245808"},{"source":"MONDO","code":"0009848","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"C562486","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0263506","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"1883","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10056961","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":89826,"name":"Rare skin disease"},"parents":[{"orpha":79382,"name":"Subcutaneous tissue disease","classifications":[187]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":{"validation_status":"y","online":"y","validation_date":"2016-06-01","source":null,"terms":[{"hpo":"HP:0001595","label":"Abnormality of the hair","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0100658","label":"Cellulitis","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0000969","label":"Edema","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0000989","label":"Pruritus","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0001581","label":"Recurrent skin infections","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0100809","label":"Scalp tenderness","frequency":"Very frequent (99-80%)","criteria":null},{"hpo":"HP:0001482","label":"Subcutaneous nodule","frequency":"Very frequent (99-80%)","criteria":null}]}}