{"orpha":33276,"name":"Kaposi sarcoma","type":"Disease","group":"Disorder","status":"active","flags":[],"synonyms":[],"definition":"A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-33276/","orphanet_url":"https://www.orpha.net/en/disease/detail/33276","names":{"fr":{"name":"Sarcome de Kaposi","synonyms":["Maladie de Kaposi"],"definition":"Tumeur vasculaire rare caractérisée par une inflammation tumorale d'origine endothéliale induite par l'Herpèsvirus humain 8 (HHV-8), dont les contextes cliniques sont très variés, apparaissant le plus souvent sous la forme de lésions cutanées ou d'atteinte des muqueuses ou des viscères."},"de":{"name":"Kaposi-Sarkom","definition":"Ein seltener vaskulärer Tumor, der sich als endotheliale entzündliche Neoplasie präsentiert, die durch das humanen Herpesvirus 8 (HHV-8) ausgelöst wird. Das klinische Bild ist außerordentlich variabel und manifestiert sich meist als kutane Läsionen oder betrifft Schleimhäute und innere Organe."},"es":{"name":"Sarcoma de Kaposi","definition":"Es un tumor vascular poco frecuente que se caracteriza por una neoplasia inflamatoria endotelial inducida por el virus del herpes humano 8 (VHH-8) que se desarrolla en entornos clínicamente distintos, manifestándose principalmente como lesiones cutáneas, o afectación de mucosas o visceras."},"it":{"name":"Sarcoma di Kaposi","definition":"Il sarcoma di Kaposi (KS) è una neoplasia infiammatoria rara dell'endotelio vascolare, causata dal virus herpes umano 8 (HHV-8), che esordisce con quadri clinici variabili, in particolare con lesioni cutanee oppure con interessamento delle muscose o dei visceri."},"nl":{"name":"Kaposi-sarcoom","definition":"Een zeldzame vasculaire tumor, gekenmerkt door endotheliaal inflammatoir neoplasma geïnduceerd door humaan herpesvirus 8 (HHV-8), met variabele klinische manifestaties, met huidlaesies als meest voorkomende, alsook mucosale of viscerale betrokkenheid."},"pt":{"name":"Sarcoma de Kaposi"},"pl":{"name":"Mięsak Kaposiego"},"cs":{"name":"Kaposiho sarkom"},"uk":{"name":"Саркома Капоші","definition":"A rare vascular tumor that is characterized by human herpes virus 8 (HHV-8)-induced endothelial inflammatory neoplasm that develops with various clinically distinct settings, manifesting mostly as cutaneous lesions, or mucosal or visceral involvement."},"zh":{"name":"卡波西肉瘤"},"tr":{"name":"Kaposi sarkomu"}},"xrefs":[{"source":"OMIM","code":"148000","qualifier":"BTNT","icd_relation":null,"validated":true},{"source":"ICD-10","code":"C46.0","qualifier":"BTNT","icd_relation":"specific","validated":true},{"source":"ICD-10","code":"C46.1","qualifier":"BTNT","icd_relation":"specific","validated":true},{"source":"ICD-10","code":"C46.2","qualifier":"BTNT","icd_relation":"specific","validated":true},{"source":"ICD-10","code":"C46.3","qualifier":"BTNT","icd_relation":"specific","validated":true},{"source":"ICD-10","code":"C46.7","qualifier":"BTNT","icd_relation":"specific","validated":true},{"source":"ICD-10","code":"C46.8","qualifier":"BTNT","icd_relation":"specific","validated":true},{"source":"ICD-10","code":"C46.9","qualifier":"BTNT","icd_relation":"specific","validated":true},{"source":"ICD-11","code":"1C60.30","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"802739943"},{"source":"ICD-11","code":"1C61.30","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"1848415584"},{"source":"ICD-11","code":"2B57","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"2131977134"},{"source":"ICD-11","code":"2B57.0","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"1617583339"},{"source":"ICD-11","code":"2B57.1","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"394490040"},{"source":"ICD-11","code":"2B57.2","qualifier":"BTNT","icd_relation":"specific","validated":true,"icd11_uri":"536268676"},{"source":"ICD-11","code":"2B57.Y","qualifier":"BTNT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"XH36A5","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"650980425"},{"source":"MONDO","code":"0005055","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D012514","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C0036220","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"6814","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10023284","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare 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