{"orpha":329341,"name":"OBSOLETE: Limbic encephalitis with DPP6 antibodies","type":"Disease","group":"Disorder","status":"inactive","flags":["Obsolete entity"],"synonyms":["OBSOLETE: Limbic encephalitis with DPPX antibodies","OBSOLETE: Limbic encephalitis with dipeptidyl-peptidase 6 antibodies"],"definition":null,"note":"This entity has been obsoleted from the Orphanet nomenclature of rare diseases.<br/><br/>Instead, consider using Autoimmune encephalitis","url":"https://raremap.alftech.space/d/ORPHA-329341/","orphanet_url":"https://www.orpha.net/en/disease/detail/329341","names":{"fr":{"name":"OBSOLETE : Encéphalite limbique avec anticorps anti-DPP6","synonyms":["OBSOLETE : Encéphalite limbique avec anticorps anti-DPPX","OBSOLETE : Encéphalite limbique avec anticorps anti-dipeptidyl-peptidase 6"]},"de":{"name":"OBSOLET: Limbische Enzephalitis mit DPP6-Antikörpern","synonyms":["OBSOLET: DPPX-Antikörper-Enzephalitis","OBSOLET: Limbische Enzephalitis mit DPPX-Antikörpern","OBSOLET: Limbische Enzephalitis mit Dipeptidylpeptidase 6-Antikörpern"]},"es":{"name":"OBSOLETO: Encefalitis límbica con anticuerpos DPP6","synonyms":["OBSOLETO: Encefalitis límbica con anticuerpos DPPX","OBSOLETO: Encefalitis límbica con anticuerpos dipeptidil-peptidasa 6"]},"it":{"name":"OBSOLETO: Encefalite limbica con anticorpi anti-DPP6","synonyms":["OBSOLETO: Encefalite limbica con anticorpi anti-DPPX","OBSOLETO: Encefalite limbica con anticorpi anti-dipeptidil-peptidasi 6"]},"nl":{"name":"OBSOLEET: Limbische encefalitis met DPP6-antilichamen","synonyms":["OBSOLEET: Limbische encefalitis met DPPX-antilichamen","OBSOLEET: Limbische encefalitis met dipeptidyl-peptidase 6-antilichamen"]},"pt":{"name":"OBSOLETO: Encefalite límbica com anticorpos DPP6"},"pl":{"name":"NIEAKTUALNE: Limbiczne zapalenie mózgu z przeciwciałami DPP6","synonyms":["NIEAKTUALNE: Limbiczne zapalenie mózgu z przeciwciałami dipeptydylo-peptydazy 6","NIEAKTUALNE: Limbiczne zapalenie mózgu z przeciwciałami DPPX"]},"cs":{"name":"NEAKTUÁLNÍ: Limbická encefalitida s DPP6 protilátkami","synonyms":["NEAKTUÁLNÍ: Limbická encefalitida s DPPX protilátkami","NEAKTUÁLNÍ: Limbická encefalitida s protilátkami dipeptidyl-peptidáza 6"]},"uk":{"name":"ЗАСТАРІЛО: Лімбічний енцефаліт з антитілами до DPP6","synonyms":["ЗАСТАРІЛО: Лімбічний енцефаліт з антитілами до дипептидилпептидази 6","ЗАСТАРІЛО: Лімбічний енцефаліт з антитілами DPPX"]},"zh":{"name":"DPP6抗体介导的边缘性脑炎","synonyms":["二肽基-6肽酶抗体介导边缘性脑炎"],"definition":"边缘性脑炎伴DPP6抗体是一种罕见的脑部炎症性疾病，其特征是亚急性或隐匿起病的各种神经学特征，包括认知功能障碍（记忆障碍、幻觉、意识混乱、健忘症）、中枢性过度兴奋（激动、震颤、肌阵挛、过度惊吓），脑干受累（吞咽困难、构音障碍、共济失调）和睡眠障碍。自主神经失调的症状包括腹泻、胃轻瘫和便秘。"},"tr":{"name":"DPP6 antikorları ile seyreden limbik ensefalit","synonyms":["DPPX antikorları ile seyreden limbik ensefalit","Dipeptidil-peptidaz 6 antikoru ile seyreden limbik ensefalit"]}},"xrefs":[],"associations":[{"type":"Referred to","orpha":622014,"name":"Autoimmune encephalitis"}],"incoming_associations":[],"preferential_parent":null,"parents":[],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}