{"orpha":289385,"name":"Malignancy diagnosed during pregnancy","type":"Particular clinical situation in a disease or syndrome","group":"Disorder","status":"active","flags":[],"synonyms":["Cancer diagnosed during pregnancy"],"definition":"A rare condition characterized by the occurrence and/or diagnosis of a malignancy during pregnancy. The most frequently diagnosed neoplasms are gynecologic tumors, especially cervical cancer, followed by hematologic malignancies. Patient management should be carried out by a multidisciplinary team of specialists.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-289385/","orphanet_url":"https://www.orpha.net/en/disease/detail/289385","names":{"fr":{"name":"Cancer diagnostiqué pendant la grossesse","definition":"Maladie rare caractérisée par l'apparition et/ou le diagnostic d'une tumeur maligne pendant la grossesse. Les tumeurs les plus fréquemment diagnostiquées sont les tumeurs gynécologiques, notamment le cancer du col de l'utérus, suivies d'hémopathies malignes. La prise en charge des patientes doit être confiée à une équipe multidisciplinaire de spécialistes."},"de":{"name":"Krebsdiagnose in der Schwangerschaft","definition":"Eine seltener Zustand, der durch das Auftreten und/oder die Diagnose einer malignen Erkrankung während der Schwangerschaft gekennzeichnet ist. Die am häufigsten diagnostizierten Neoplasien sind gynäkologische Tumore, insbesondere Gebärmutterhalskrebs, gefolgt von hämatologischen Malignomen. Die Behandlung der Patientin sollte von einem multidisziplinären Team von Spezialisten durchgeführt werden."},"es":{"name":"Cáncer diagnosticado durante el embarazo","definition":"Es un trastorno poco frecuente caracterizado por el desarrollo y/o diagnóstico de una neoplasia maligna durante el embarazo. Las neoplasias diagnosticadas con mayor frecuencia son los tumores ginecológicos, especialmente el cáncer de cuello uterino, seguidos de las neoplasias hematológicas. El manejo de las pacientes debe ser realizado por un equipo multidisciplinar de especialistas."},"it":{"name":"Tumore maligno diagnosticato in gravidanza","synonyms":["Cancro diagnosticato in gravidanza"]},"nl":{"name":"Maligne tumor gediagnosticeerd tijdens zwangerschap","synonyms":["Kanker gediagnosticeerd tijdens zwangerschap","Kwaadaardige tumor gediagnosticeerd tijdens de zwangerschap"],"definition":"Een zeldzame aandoening, gekenmerkt door voorkomen en/of diagnose van een maligne tumor tijdens de zwangerschap. Neoplasmata die het vaakst gediagnosticeerd worden, zijn gynaecologische tumoren, vooral kanker van baarmoederhals, gevolgd door hematologische maligniteiten. Ziektebeheer van een patiënt dient uitgevoerd te worden door een multidisciplinair team van specialisten."},"pt":{"name":"Cancro diagnosticado durante a gravidez","definition":"Patologia rara caracterizada pela ocorrência e/ou diagnóstico de uma doença maligna durante a gravidez. As neoplasias mais frequentemente diagnosticadas são os tumores ginecológicos, especialmente o cancro cervical, seguidos das neoplasias hematológicas. O seguimento clínico deve ser realizado por uma equipa multidisciplinar de especialistas."},"pl":{"name":"Nowotwór złośliwy zdiagnozowany podczas ciąży","synonyms":["Rak zdiagnozowany podczas ciąży"],"definition":"Rzadko występujący stan, charakteryzujący się wystąpieniem i/lub rozpoznaniem nowotworu złośliwego w czasie ciąży. Najczęściej rozpoznawanymi nowotworami są nowotwory układu moczowo-płciowego, zwłaszcza rak szyjki macicy, a w dalszej kolejności nowotwory układu krwiotwórczego. Opieką nad pacjentem powinien zajmować się multidyscyplinarny zespół specjalistów."},"cs":{"name":"Malignity diagnostikované během těhotenství","synonyms":["Nádory diagnostikované během těhotenství"]},"uk":{"name":"Злоякісне новоутворення, діагностоване під час вагітності","synonyms":["Рак, діагностований під час вагітності"],"definition":"A rare condition characterized by the occurrence and/or diagnosis of a malignancy during pregnancy. The most frequently diagnosed neoplasms are gynecologic tumors, especially cervical cancer, followed by hematologic malignancies. Patient management should be carried out by a multidisciplinary team of specialists."},"zh":{"name":"妊娠期间诊断为恶性肿瘤","synonyms":["怀孕期间确诊恶性肿瘤"]},"tr":{"name":"Hamilelik sırasında teşhis edilen habis durum","synonyms":["Gebelik sırasında teşhis edilen kanser"]}},"xrefs":[{"source":"ICD-10","code":"O99.8","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"JB64.Y","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"MONDO","code":"0017330","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679948","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":96344,"name":"Rare gynecologic or obstetric disease"},"parents":[{"orpha":163637,"name":"Rare disorder related with pregnancy, childbirth and puerperium","classifications":[205]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}