{"orpha":284362,"name":"Fetal lung interstitial tumor","type":"Clinical subtype","group":"Subtype of disorder","status":"active","flags":[],"synonyms":["FLIT","Immature interstitial mesenchymal tumor"],"definition":null,"note":null,"url":"https://raremap.alftech.space/d/ORPHA-284362/","orphanet_url":"https://www.orpha.net/en/disease/detail/284362","names":{"fr":{"name":"Tumeur interstitielle du poumon foetal","synonyms":["FLIT","Tumeur interstitielle mésenchymateuse immature"]},"de":{"name":"Fetaler Lungentumor, interstitieller","synonyms":["FLIT","Tumor, interstitieller mesenchymaler unreifer"]},"es":{"name":"Tumor intersticial del pulmón fetal","synonyms":["FLIT","Tumor intersticial mesenquimal inmaduro"]},"it":{"name":"Tumore polmonare interstiziale fetale","synonyms":["FLIT","Tumore mesenchimale interstiziale immaturo"]},"nl":{"name":"Interstitiële tumor van foetale long","synonyms":["FLIT","Onvolgroeide interstitiële mesenchymale tumor"]},"pt":{"name":"Tumor intersticial do pulmão, fetal"},"pl":{"name":"Śródmiąższowy nowotwór płuc płodu","synonyms":["FLIT","Immature interstitial mesenchymal tumor"]},"cs":{"name":"Fetální plicní intersticiální nádory","synonyms":["FLIT","Nezralé intersticiální mezenchymální nádory"]},"uk":{"name":"Інтерстиціальна пухлина легень плода","synonyms":["FLIT","Незріла інтерстиціальна мезенхімальна пухлина"]},"zh":{"name":"胎肺间质肿瘤","synonyms":["未成熟间质间叶细胞肿瘤"]},"tr":{"name":"Fetal akciğer interstisyel tümörü","synonyms":["FLIT","İmmatür interstisyel mezenkimal tümör"]}},"xrefs":[{"source":"ICD-10","code":"D14.3","qualifier":"NTBT","icd_relation":"attributed","validated":true},{"source":"ICD-11","code":"LA75.Y","qualifier":"NTBT","icd_relation":"index","validated":true,"icd11_uri":"1939904626"},{"source":"MONDO","code":"0017289","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C5679952","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":250908,"name":"Rare neoplastic disease"},"parents":[{"orpha":64742,"name":"Pleuropulmonary blastoma","classifications":[184,202]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":["Infancy","Neonatal"],"prevalence":[],"phenotypes":null}