{"orpha":284264,"name":"IgG4-related disease","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["IgG4-related sclerosing disease","Immunoglobulin G4-related sclerosing disease"],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-284264/","orphanet_url":"https://www.orpha.net/en/disease/detail/284264","names":{"fr":{"name":"Maladie associée aux IgG4","synonyms":["Maladie sclérosante liée aux IgG4","Maladie sclérosante liée aux immunoglobulines G4"]},"de":{"name":"IgG4-assoziierte Krankheit","synonyms":["Immunglobulin-G4-assoziierte sklerosierende Krankheit","IgG4-assoziierte Systemkrankheit","IgG4-assoziierte sklerosierende Krankheit"]},"es":{"name":"Enfermedad asociada a IgG4","synonyms":["Enfermedad esclerosante ligada a inmunoglobulinas G4"]},"it":{"name":"Malattia IgG4-correlata","synonyms":["Malattia sclerosante legata alle IgG4","Malattia sclerosante legata alle immunoglobuline G4","Malattia sistemica legata alle IgG4"]},"nl":{"name":"IgG4-gerelateerde ziekte","synonyms":["IgG4-gerelateerde scleroserende ziekte","IgG4-gerelateerde systemische ziekte","Immunoglobuline G4-gerelateerde scleroserende ziekte"]},"pt":{"name":"Doença IgG4-relacionada","synonyms":["Doença esclerosante relacionada com imunoglobulina G4"]},"pl":{"name":"Choroba stwardniająca związana z immunoglobuliną G4","synonyms":["Choroba stwardniająca związana z IgG4","Choroba układowa związana z IgG4"]},"cs":{"name":"IgG4 asociovaná onemocnění","synonyms":["IgG4 asociovaná sklerotizující onemocnění","IgG4 asociovaná systémová onemocnění","Imunoglobulin G4 asociovaná sklerotizující onemocnění"]},"uk":{"name":"Захворювання, повязане з IgG4","synonyms":["Склерозуюча хвороба, повязана з IgG4","Імуноглобулін G4 асоційована склерозуюча хвороба"]},"zh":{"name":"IgG4相关疾病","synonyms":["免疫球蛋白G4相关硬化性疾病"]},"tr":{"name":"IgG4-ilişkili hastalık","synonyms":["IgG4-ilişkili sistemik hastalık","IgG4-ilişkili sklerozan hastalık","İmmünoglobulin G4-ilişkili sklerozan hastalık"]}},"xrefs":[{"source":"ICD-11","code":"4A43.0","qualifier":"E","icd_relation":"specific","validated":true,"icd11_uri":"99883782"},{"source":"MONDO","code":"17287","qualifier":"E","icd_relation":null,"validated":true},{"source":"MeSH","code":"D000077733","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C3203653","qualifier":"E","icd_relation":null,"validated":true},{"source":"GARD","code":"12521","qualifier":"E","icd_relation":null,"validated":true},{"source":"MedDRA","code":"10071569","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98023,"name":"Rare systemic or rheumatologic disease"},"parents":[{"orpha":182228,"name":"Systemic autoimmune disease","classifications":[196]}],"children":[{"orpha":451607,"name":"Cutaneous pseudolymphoma","type":"Disease"},{"orpha":449566,"name":"Eosinophilic angiocentric fibrosis","type":"Disease"},{"orpha":596448,"name":"IgG4-related systemic disease","type":"Disease"},{"orpha":555437,"name":"Lymphoplasmacytic inflammatory pseudotumor of the liver","type":"Clinical subtype"},{"orpha":451602,"name":"Primary cutaneous plasmacytosis","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":["Not applicable"],"onset":["Adult"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Not yet validated","source":"ORPHANET"}],"phenotypes":null}