{"orpha":276061,"name":"Genetic frontotemporal degeneration with dementia","type":"Category","group":"Group of disorders","status":"active","flags":[],"synonyms":[],"definition":null,"note":"This term does not characterize a disease but a group of diseases. To learn about the diseases included under this term, you can consult the classifications.","url":"https://raremap.alftech.space/d/ORPHA-276061/","orphanet_url":"https://www.orpha.net/en/disease/detail/276061","names":{"fr":{"name":"Dégénérescence fronto-temporale génétique avec démence"},"de":{"name":"Frontotemporale Degeneration mit Demenz, genetisch bedingte"},"es":{"name":"Degeneración frontotemporal genética con demencia"},"it":{"name":"Degenerazione frontotemporale genetica con demenza"},"nl":{"name":"Genetische frontotemporale degeneratie met dementie"},"pt":{"name":"Degeneração frontotemporal genética com demência"},"pl":{"name":"Zwyrodnienie czołowo-skroniowe z otępieniem uwarunkowane genetycznie"},"cs":{"name":"Dědičná frontotemporální degenerace s demencí"},"uk":{"name":"Генетично обумовлена лобно-скронева дегенерація з деменцією"},"zh":{"name":"遗传性额颞叶变性伴痴呆"},"tr":{"name":"Demans ile seyreden genetik frontotemporal dejenerasyon"}},"xrefs":[{"source":"UMLS","code":"C5680752","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":98006,"name":"Rare neurologic disease"},"parents":[{"orpha":276058,"name":"Genetic neurodegenerative disease with dementia","classifications":[156]}],"children":[{"orpha":282,"name":"Frontotemporal dementia","type":"Clinical group"},{"orpha":275872,"name":"Frontotemporal dementia with motor neuron disease","type":"Disease"},{"orpha":52430,"name":"Inclusion body myopathy with Paget disease of bone and frontotemporal dementia","type":"Disease"},{"orpha":683,"name":"Progressive supranuclear palsy","type":"Disease"}],"genes":[],"genes_via_subtypes":[],"inheritance":[],"onset":[],"prevalence":[],"phenotypes":null}