{"orpha":275828,"name":"Pulmonary arterial hypertension associated with chronic hemolytic anemia","type":"Clinical group","group":"Group of disorders","status":"active","flags":[],"synonyms":["PAH associated with chronic hemolytic anemia"],"definition":"Pulmonary arterial hypertension associated with chronic hemolytic anemia (PAH-CHA) is a form of PAH characterized by an elevated pulmonary arterial resistance leading to right heart failure observed as a complication of chronic hemolytic anemia.","note":null,"url":"https://raremap.alftech.space/d/ORPHA-275828/","orphanet_url":"https://www.orpha.net/en/disease/detail/275828","names":{"fr":{"name":"Hypertension artérielle pulmonaire associée à une anémie hémolytique chronique","synonyms":["HTAP associée à une anémie hémolytique chronique"],"definition":"Forme d'HTAP caractérisée par une résistance artérielle pulmonaire élevée entraînant une insuffisance cardiaque droite observée comme complication d'une anémie hémolytique chronique."},"de":{"name":"Pulmonale arterielle Hypertonie mit assoziierter chronisch-hämolytischer Anämie","synonyms":["PAH mit assoziierter chronischer hämolytischer Anämie"]},"es":{"name":"Hipertensión arterial pulmonar asociada a anemia hemolítica crónica","synonyms":["HAP asociada a anemia hemolítica crónica"],"definition":"La hipertensión arterial pulmonar asociada con anemia hemolítica crónica (HAP-CHA) es una forma de hipertensión arterial pulmonar (HAP) caracterizada por una resistencia arterial pulmonar elevada que conduce a insuficiencia cardíaca derecha observada como una complicación de la anemia hemolítica crónica."},"it":{"name":"Ipertensione arteriosa polmonare associata ad anemia emolitica cronica","synonyms":["PAH associata ad anemia emolitica cronica"]},"nl":{"name":"Pulmonale arteriële hypertensie geassocieerd met chronische hemolytische anemie","synonyms":["PAH geassocieerd met chronische hemolytische anemie"],"definition":"'Pulmonale arteriële hypertensie geassocieerd met chronische hemolytische anemie (PAH-CHA) is een vorm van pulmonale arteriële hypertensie (PAH; zie deze term) die wordt gekarakteriseerd door een verhoogde weerstand in de longslagaders die wordt waargenomen als een complicatie van chronische hemolytische anemie en die leidt tot een falen van de rechterzijde van het hart.'"},"pt":{"name":"Hipertensão arterial pulmonar associada a anemia hemolítica crónica"},"pl":{"name":"Płucne nadciśnienie tętnicze związane z przewlekłą niedokrwistością hemolityczną","synonyms":["PAH związane z przewlekłą niedokrwistością hemolityczną"]},"cs":{"name":"Plicní arteriální hypertenze asociovaná s chronickou hemolytickou anémií","synonyms":["PAH asociovaná s chronickou hemolytickou anémií"]},"uk":{"name":"Легенева артеріальна гіпертензія, асоційована з хронічною гемолітичною анемією","synonyms":["ЛАГ, повязана з хронічною гемолітичною анемією"],"definition":"Pulmonary arterial hypertension associated with chronic hemolytic anemia (PAH-CHA) is a form of PAH (see this term) characterized by an elevated pulmonary arterial resistance leading to right heart failure observed as a complication of chronic hemolytic anemia."},"zh":{"name":"慢性溶血性贫血相关肺动脉高压","synonyms":["慢性溶血性贫血相关PAH"],"definition":"肺动脉高压合并慢性溶血性贫血(PAH-CHA)是一种肺动脉高压(见该词条)，其特征是肺动脉阻力升高导致右心衰竭，被认为是慢性溶血性贫血的并发症。"},"tr":{"name":"Kronik hemolitik anemi ilişkili pulmoner arteriyel hipertansiyon","synonyms":["Kronik hemolitik anemi ile ilişkili PAH"]}},"xrefs":[{"source":"MONDO","code":"17156","qualifier":"E","icd_relation":null,"validated":true},{"source":"UMLS","code":"C3698315","qualifier":"E","icd_relation":null,"validated":true}],"associations":[],"incoming_associations":[],"preferential_parent":{"orpha":97955,"name":"Rare respiratory disease"},"parents":[{"orpha":275791,"name":"Pulmonary arterial hypertension associated with another disease","classifications":[184,233]}],"children":[],"genes":[],"genes_via_subtypes":[],"inheritance":["Multigenic/multifactorial","Not applicable"],"onset":["All ages"],"prevalence":[{"type":"Point prevalence","qualification":"Class only","class":"Unknown","value":0.0,"area":"Worldwide","status":"Validated","source":"ORPHANET"}],"phenotypes":null}